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N01.1 ICD-10-CM Code: Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

N01.1 is not a CMS-HCC payment code. MEAT criteria · RAF calculator status · HCC Buddy coding tools

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FY 2026 Apr update / Diseases of the genitourinary system (N00-N99) / Glomerular diseases (N00-N08)

N01.1

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

A rapidly worsening kidney condition where the filtering units develop focal and segmental scarring and damage, causing blood and protein to leak into the urine.

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

N/A

Not mapped

ACA/HHS

N/A

Not mapped

ESRD/PACE

N/A

Not mapped

RXHCC

N/A

Not mapped

Code Book Path

Official
N01Rapidly progressive nephritic syndrome
N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

Inclusion Terms

Official
  • Rapidly progressive nephritic syndrome with focal and segmental hyalinosis
  • Rapidly progressive nephritic syndrome with focal and segmental sclerosis
  • Rapidly progressive nephritic syndrome with focal glomerulonephritis

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for N01.1 in this effective period.

Related Child Codes

Official
N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis

Includes

Official
  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Excludes 1

Official
  • nephritic syndrome NOS (N05.-)

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for N01.1 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for N01.1 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for N01.1 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance
This code specifies the morphologic pattern seen on kidney biopsy; ensure biopsy results are documented before coding
Verify the 'rapidly progressive' nature is clinically confirmed with rising creatinine and declining GFR over weeks to months

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Is N01.1 an HCC code?

No. N01.1 is a billable ICD-10-CM code but does not map to any HCC category in V28, V24, ESRD, or RxHCC.

Code
N01.1
Description
Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
HCC (V28)
No CMS-HCC V28 mapping
RAF reference coefficient
Billable
Yes
Payment year
2026

Coder workflow notes

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This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).

What This Code Means

N01.1 is the ICD-10-CM diagnosis code for rapidly progressive nephritic syndrome with focal and segmental glomerular lesions. A rapidly worsening kidney condition where the filtering units develop focal and segmental scarring and damage, causing blood and protein to leak into the urine. N01.1 sits in the ICD-10-CM chapter for diseases of the genitourinary system (n00-n99), within the section covering glomerular diseases (n00-n08).

N01.1 is a billable ICD-10-CM code, but the current payload does not show a mapping under the CMS-HCC V28, V24, ESRD, or RxHCC models. Do not assign risk adjustment value from this page when no source-backed mapping is shown; verify the applicable model and payment year.

This code specifies the morphologic pattern seen on kidney biopsy; ensure biopsy results are documented before coding.

HCC Buddy maintains structured V28 and V24 mapping, source-labeled coefficient references, and MEAT documentation criteria for N01.1 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • This code specifies the morphologic pattern seen on kidney biopsy; ensure biopsy results are documented before coding
  • Verify the 'rapidly progressive' nature is clinically confirmed with rising creatinine and declining GFR over weeks to months

Child Codes

Code Hierarchy

N01Rapidly progressive nephritic syndromeN01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

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