Skip to content

N01 ICD-10-CM Code: Rapidly progressive nephritic syndrome

N01 is not a CMS-HCC payment code. MEAT criteria · RAF calculator status · free HCC coding tools

ICD-10-CM Code View

HCC Buddy Code Card

Digital ICD-10 code-book layout with official code detail, always-visible risk models, Code Trumping, and Buddy coding guidance.

FY 2026 Apr update / Diseases of the genitourinary system (N00-N99) / Glomerular diseases (N00-N08)

N01

Header CodeICD-10-CMOfficial ICD-10-CMCodebook guidance

Rapidly progressive nephritic syndrome

Rapidly progressive nephritic syndrome

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

N/A

Not mapped

ACA/HHS

N/A

Not mapped

ESRD/PACE

N/A

Not mapped

RXHCC

N/A

Not mapped

Code Book Path

Official
N0Glomerular diseases (N00-N08)
N01Rapidly progressive nephritic syndrome

Inclusion Terms

Official

ICD-10-CM does not list inclusion terms for N01 in this effective period.

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for N01 in this effective period.

Related Child Codes

Official
N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis

Includes

Official
  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Excludes 1

Official
  • nephritic syndrome NOS (N05.-)

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for N01 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for N01 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for N01 in this effective period.

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Code
N01
Description
Rapidly progressive nephritic syndrome
HCC (V28)
No CMS-HCC V28 mapping
RAF reference coefficient
Billable
No
Payment year
2026

Coder workflow notes

Get the V28 mapping + MEAT cheat sheet

One printable reference: check representative V28 mappings and the documentation reminders your note needs. Free, no card.

Free PDF. No card. Unsubscribe anytime.

What This Code Means

N01 is the ICD-10-CM diagnosis code for rapidly progressive nephritic syndrome. N01 sits in the ICD-10-CM chapter for diseases of the genitourinary system (n00-n99), within the section covering glomerular diseases (n00-n08).

Header codes like N01 cannot be reported on claims directly; they organize child codes that share clinical context. Coders should select the billable child code that matches the documented presentation and then verify its current source-backed HCC mapping. Do not infer a child code or risk adjustment value from the header alone.

HCC Buddy maintains structured V28 and V24 mapping, source-labeled coefficient references, and MEAT documentation criteria for N01 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Includes

  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Excludes 1, Do NOT code together

  • nephritic syndrome NOS (N05.-)

Child Codes

Code Hierarchy

N01Rapidly progressive nephritic syndrome
N01Rapidly progressive nephritic syndrome

Work N01 in HCC Buddy

Open N01 in the Code Book for the full Index-to-Tabular path, MEAT checklist, and V28 HCC mapping, or in the Encoder to code from a keyword search. Pro includes 7 days to try everything, no card required.