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Q33.0 ICD-10-CM Code: Congenital cystic lung

Q33.0 is not a CMS-HCC payment code. MEAT criteria · RAF calculator · HCC coding software

ICD-10-CM Code View

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FY 2026 Apr update / Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0) / Congenital malformations of the respiratory system (Q30-Q34)

Q33.0

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Congenital cystic lung

A birth defect where the lung contains one or more fluid-filled sacs (cysts) instead of normal lung tissue, which may affect breathing and oxygen exchange.

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

N/A

Not mapped

ACA/HHS

N/A

Not mapped

ESRD/PACE

N/A

Not mapped

RXHCC

N/A

Not mapped

Code Book Path

Official
Q33Congenital malformations of lung
Q33.0Congenital cystic lung

Inclusion Terms

Official
  • Congenital cystic lung disease
  • Congenital honeycomb lung
  • Congenital polycystic lung disease

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for Q33.0 in this effective period.

Related Child Codes

Official
Q33.1Accessory lobe of lung
Q33.2Sequestration of lung
Q33.3Agenesis of lung
Q33.4Congenital bronchiectasis
Q33.5Ectopic tissue in lung

Includes

Official

ICD-10-CM does not list Includes notes for Q33.0 in this effective period.

Excludes 1

Official
  • cystic fibrosis (E84.0)
  • cystic lung disease, acquired or unspecified (J98.4)

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for Q33.0 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for Q33.0 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for Q33.0 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance
Congenital cystic lung may require imaging confirmation; ensure radiology reports are reviewed
Code any associated respiratory complications or infections separately

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Is Q33.0 an HCC code?

No. Q33.0 is a billable ICD-10-CM code but does not map to any HCC category in V28, V24, ESRD, or RxHCC.

Code
Q33.0
Description
Congenital cystic lung
HCC (V28)
No CMS-HCC V28 mapping
RAF
Billable
Yes
Payment year
2026

Coder workflow notes

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This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).

What This Code Means

Q33.0 is the ICD-10-CM diagnosis code for congenital cystic lung. A birth defect where the lung contains one or more fluid-filled sacs (cysts) instead of normal lung tissue, which may affect breathing and oxygen exchange. Q33.0 sits in the ICD-10-CM chapter for congenital malformations, deformations and chromosomal abnormalities (q00-qa0), within the section covering congenital malformations of the respiratory system (q30-q34).

Q33.0 is a billable ICD-10-CM code but does not map to a payment HCC under the CMS-HCC V28, V24, ESRD, or RxHCC risk adjustment models. It can be reported on Medicare Advantage encounter data submissions but it does not contribute to a beneficiary's RAF score and therefore does not affect risk-adjusted payments to the plan.

Congenital cystic lung may require imaging confirmation; ensure radiology reports are reviewed.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for Q33.0 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • Congenital cystic lung may require imaging confirmation; ensure radiology reports are reviewed
  • Code any associated respiratory complications or infections separately

Excludes 1, Do NOT code together

  • cystic fibrosis (E84.0)
  • cystic lung disease, acquired or unspecified (J98.4)

Child Codes

Code Hierarchy

Work Q33.0 in HCC Buddy

Open Q33.0 in the Code Book for the full Index-to-Tabular path, MEAT checklist, and V28 HCC mapping, or in the Encoder to code from a keyword search. Pro includes 7 days to try everything, no card required.