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N04 ICD-10-CM Code: Nephrotic syndrome

ICD-10-CM Code View

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FY 2026 Apr update / Diseases of the genitourinary system (N00-N99) / Glomerular diseases (N00-N08)

N04

Header CodeICD-10-CMOfficial ICD-10-CMCodebook guidance

Nephrotic syndrome

Nephrotic syndrome

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

N/A

Not mapped

ACA/HHS

N/A

Not mapped

ESRD/PACE

N/A

Not mapped

RXHCC

N/A

Not mapped

Code Book Path

Official
N0Glomerular diseases (N00-N08)
N04Nephrotic syndrome

Inclusion Terms

Official

ICD-10-CM does not list inclusion terms for N04 in this effective period.

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for N04 in this effective period.

Related Child Codes

Official
N04.0Nephrotic syndrome with minor glomerular abnormality
N04.1Nephrotic syndrome with focal and segmental glomerular lesions
N04.2Nephrotic syndrome with diffuse membranous glomerulonephritis
N04.3Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
N04.4Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis

Includes

Official
  • congenital nephrotic syndrome
  • lipoid nephrosis

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for N04 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for N04 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for N04 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for N04 in this effective period.

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Code
N04
Description
Nephrotic syndrome
HCC (V28)
No CMS-HCC V28 mapping
RAF
Billable
No
Payment year
2026

Coder workflow notes

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What This Code Means

N04 is the ICD-10-CM diagnosis code for nephrotic syndrome. N04 sits in the ICD-10-CM chapter for diseases of the genitourinary system (n00-n99), within the section covering glomerular diseases (n00-n08).

Header codes like N04 cannot be reported on claims directly, they organize child codes that share clinical context but the actual diagnosis must be coded to the highest level of specificity supported by the documentation. Coders should look at N04's child codes and select the one that matches the patient's documented presentation, since payers reject header codes submitted as the primary diagnosis. For risk adjustment workflows, header codes never contribute to a Medicare Advantage member's RAF score on their own; only billable child codes that happen to map to a payment HCC affect risk-adjusted plan payments.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for N04 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Includes

  • congenital nephrotic syndrome
  • lipoid nephrosis

Child Codes

Code Hierarchy

N04Nephrotic syndrome
N04Nephrotic syndrome

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