Congenital malformations, deformations and chromosomal abnormalities
ICD-10-CM Chapter 17 (Q00-QA0) in the FY2026 code set. 74 codes in this chapter map to a CMS-HCC V28 payment category, across 4 HCC categories.
CMS-HCC V28 categories in this chapter (4)
Open any category for its full member-code list, RAF, and hierarchy.
Risk-adjusting ICD-10-CM codes (74)
Codes in this chapter that map to a CMS-HCC V28 payment category. Open any code for its full detail.
- Q00.0Anencephaly
- Q00.1Craniorachischisis
- Q00.2Iniencephaly
- Q01.0Frontal encephalocele
- Q01.1Nasofrontal encephalocele
- Q01.2Occipital encephalocele
- Q01.8Encephalocele of other sites
- Q01.9Encephalocele, unspecified
- Q02Microcephaly
- Q03.0Malformations of aqueduct of Sylvius
- Q03.1Atresia of foramina of Magendie and Luschka
- Q03.8Other congenital hydrocephalus
- Q03.9Congenital hydrocephalus, unspecified
- Q04.0Congenital malformations of corpus callosum
- Q04.1Arhinencephaly
- Q04.2Holoprosencephaly
- Q04.3Other reduction deformities of brain
- Q04.4Septo-optic dysplasia of brain
- Q04.5Megalencephaly
- Q04.6Congenital cerebral cysts
- Q04.8Other specified congenital malformations of brain
- Q04.9Congenital malformation of brain, unspecified
- Q05.0Cervical spina bifida with hydrocephalus
- Q05.1Thoracic spina bifida with hydrocephalus
- Q05.2Lumbar spina bifida with hydrocephalus
- Q05.3Sacral spina bifida with hydrocephalus
- Q05.4Unspecified spina bifida with hydrocephalus
- Q05.5Cervical spina bifida without hydrocephalus
- Q05.6Thoracic spina bifida without hydrocephalus
- Q05.7Lumbar spina bifida without hydrocephalus
- Q05.8Sacral spina bifida without hydrocephalus
- Q05.9Spina bifida, unspecified
- Q06.0Amyelia
- Q06.1Hypoplasia and dysplasia of spinal cord
- Q06.2Diastematomyelia
- Q06.3Other congenital cauda equina malformations
- Q06.4Hydromyelia
- Q06.8Other specified congenital malformations of spinal cord
- Q06.9Congenital malformation of spinal cord, unspecified
- Q07.00Arnold-Chiari syndrome without spina bifida or hydrocephalus
- Q07.01Arnold-Chiari syndrome with spina bifida
- Q07.02Arnold-Chiari syndrome with hydrocephalus
- Q07.03Arnold-Chiari syndrome with spina bifida and hydrocephalus
- Q07.8Other specified congenital malformations of nervous system
- Q07.9Congenital malformation of nervous system, unspecified
- Q40.0Congenital hypertrophic pyloric stenosis
- Q41.0Congenital absence, atresia and stenosis of duodenum
- Q41.1Congenital absence, atresia and stenosis of jejunum
- Q41.2Congenital absence, atresia and stenosis of ileum
- Q41.8Congenital absence, atresia and stenosis of other specified parts of small intestine
- Q41.9Congenital absence, atresia and stenosis of small intestine, part unspecified
- Q42.0Congenital absence, atresia and stenosis of rectum with fistula
- Q42.1Congenital absence, atresia and stenosis of rectum without fistula
- Q42.2Congenital absence, atresia and stenosis of anus with fistula
- Q42.3Congenital absence, atresia and stenosis of anus without fistula
- Q42.8Congenital absence, atresia and stenosis of other parts of large intestine
- Q42.9Congenital absence, atresia and stenosis of large intestine, part unspecified
- Q43.1Hirschsprung's disease
- Q43.2Other congenital functional disorders of colon
- Q43.3Congenital malformations of intestinal fixation
- Q44.2Atresia of bile ducts
- Q44.3Congenital stenosis and stricture of bile ducts
- Q44.71Alagille syndrome
- Q85.00Neurofibromatosis, unspecified
- Q85.01Neurofibromatosis, type 1
- Q85.02Neurofibromatosis, type 2
- Q85.03Schwannomatosis
- Q85.09Other neurofibromatosis
- Q85.1Tuberous sclerosis
- Q85.81PTEN hamartoma tumor syndrome
- Q85.82Other Cowden syndrome
- Q85.83Von Hippel-Lindau syndrome
- Q85.89Other phakomatoses, not elsewhere classified
- Q85.9Phakomatosis, unspecified
Frequently asked questions
How many ICD-10-CM codes in Congenital malformations, deformations and chromosomal abnormalities risk-adjust under CMS-HCC V28?
74 ICD-10-CM codes in the Q00-QA0 chapter (Congenital malformations, deformations and chromosomal abnormalities) map to a CMS-HCC V28 payment category for payment year 2026.
Which CMS-HCC V28 categories do Q00-QA0 codes map to?
Codes in this chapter map to 4 distinct CMS-HCC V28 categories, most commonly HCC 182 (Spinal Cord Disorders/Injuries), HCC 78 (Intestinal Obstruction/Perforation), HCC 23 (Prostate, Breast, and Other Cancers and Tumors).
What ICD-10-CM chapter is Q00-QA0?
Q00-QA0 is ICD-10-CM Chapter 17, Congenital malformations, deformations and chromosomal abnormalities, in the FY2026 code set.
Source: FY2026 ICD-10-CM Tabular (CDC/NCHS) and the CMS-HCC v28 PY2026 mapping file.