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Q01 ICD-10-CM Code: Encephalocele

ICD-10-CM Code View

HCC Buddy Code Card

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FY 2026 Apr update / Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0) / Congenital malformations of the nervous system (Q00-Q07)

Q01

Header CodeICD-10-CMOfficial ICD-10-CMCodebook guidance

Encephalocele

Encephalocele

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

N/A

Not mapped

ACA/HHS

N/A

Not mapped

ESRD/PACE

N/A

Not mapped

RXHCC

N/A

Not mapped

Code Book Path

Official
Q0Congenital malformations of the nervous system (Q00-Q07)
Q01Encephalocele

Inclusion Terms

Official

ICD-10-CM does not list inclusion terms for Q01 in this effective period.

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for Q01 in this effective period.

Related Child Codes

Official
Q01.0Frontal encephalocele
Q01.1Nasofrontal encephalocele
Q01.2Occipital encephalocele
Q01.8Encephalocele of other sites
Q01.9Encephalocele, unspecified

Includes

Official
  • Arnold-Chiari syndrome, type III
  • encephalocystocele
  • encephalomyelocele
  • hydroencephalocele
  • hydromeningocele, cranial

Excludes 1

Official
  • Meckel-Gruber syndrome (Q61.9)

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for Q01 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for Q01 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for Q01 in this effective period.

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Coder workflow notes

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What This Code Means

Q01 is the ICD-10-CM diagnosis code for encephalocele. Q01 sits in the ICD-10-CM chapter for congenital malformations, deformations and chromosomal abnormalities (q00-qa0), within the section covering congenital malformations of the nervous system (q00-q07).

Header codes like Q01 cannot be reported on claims directly, they organize child codes that share clinical context but the actual diagnosis must be coded to the highest level of specificity supported by the documentation. Coders should look at Q01's child codes and select the one that matches the patient's documented presentation, since payers reject header codes submitted as the primary diagnosis. For risk adjustment workflows, header codes never contribute to a Medicare Advantage member's RAF score on their own; only billable child codes that happen to map to a payment HCC affect risk-adjusted plan payments.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for Q01 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Includes

  • Arnold-Chiari syndrome, type III
  • encephalocystocele
  • encephalomyelocele
  • hydroencephalocele
  • hydromeningocele, cranial
  • meningocele, cerebral
  • meningoencephalocele

Excludes 1, Do NOT code together

  • Meckel-Gruber syndrome (Q61.9)

Child Codes

Code Hierarchy

Q01Encephalocele
Q01Encephalocele

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