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E00 ICD-10-CM Code: Congenital iodine-deficiency syndrome

ICD-10-CM Code View

HCC Buddy Code Card

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FY 2026 Apr update / Endocrine, nutritional and metabolic diseases (E00-E89) / Disorders of thyroid gland (E00-E07)

E00

Header CodeICD-10-CMOfficial ICD-10-CMCodebook guidance

Congenital iodine-deficiency syndrome

Congenital iodine-deficiency syndrome

CMS-HCC V28

0

0

RAF 0

CMS-HCC V24

0

0

RAF 0

ACA/HHS

0

0

RAF 0

ESRD/PACE

0

0

RAF 0

RXHCC

0

0

RAF 0

Code Trumping

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Code Book Path

Official
E0Disorders of thyroid gland (E00-E07)
E00Congenital iodine-deficiency syndrome

Inclusion Terms

Official

ICD-10-CM does not list inclusion terms for E00 in this effective period.

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for E00 in this effective period.

Related Child Codes

Official
E00.0Congenital iodine-deficiency syndrome, neurological type
E00.1Congenital iodine-deficiency syndrome, myxedematous type
E00.2Congenital iodine-deficiency syndrome, mixed type
E00.9Congenital iodine-deficiency syndrome, unspecified

Includes

Official

ICD-10-CM does not list Includes notes for E00 in this effective period.

Excludes 1

Official
  • subclinical iodine-deficiency hypothyroidism (E02)

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for E00 in this effective period.

Use Additional

Official
  • code (F70-F79) to identify associated intellectual disabilities.

Code Also

Official

ICD-10-CM does not list Code Also instructions for E00 in this effective period.

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Coder workflow notes

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What This Code Means

E00 is the ICD-10-CM diagnosis code for congenital iodine-deficiency syndrome. E00 sits in the ICD-10-CM chapter for endocrine, nutritional and metabolic diseases (e00-e89), within the section covering disorders of thyroid gland (e00-e07).

Header codes like E00 cannot be reported on claims directly, they organize child codes that share clinical context but the actual diagnosis must be coded to the highest level of specificity supported by the documentation. Coders should look at E00's child codes and select the one that matches the patient's documented presentation, since payers reject header codes submitted as the primary diagnosis. For risk adjustment workflows, header codes never contribute to a Medicare Advantage member's RAF score on their own; only billable child codes that happen to map to a payment HCC affect risk-adjusted plan payments.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for E00 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Excludes 1, Do NOT code together

  • subclinical iodine-deficiency hypothyroidism (E02)

Use Additional Code

  • code (F70-F79) to identify associated intellectual disabilities.

Child Codes

Code Hierarchy

E00Congenital iodine-deficiency syndrome
E00Congenital iodine-deficiency syndrome

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