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QA0.01 ICD-10-CM Code: Neurodevelopmental disorders related to pathogenic variants in certain specific genes

ICD-10-CM Code View

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FY 2026 Apr update / Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0) / Genetic disorders, not elsewhere classified (QA0)

QA0.01

Header CodeICD-10-CMOfficial ICD-10-CMCodebook guidance

Neurodevelopmental disorders related to pathogenic variants in certain specific genes

Neurodevelopmental disorders related to pathogenic variants in certain specific genes

CMS-HCC V28

N/A

Not mapped

CMS-HCC V24

N/A

Not mapped

ACA/HHS

N/A

Not mapped

ESRD/PACE

N/A

Not mapped

RXHCC

N/A

Not mapped

Code Book Path

Official
QA0Neurodevelopmental disorders related to specific genetic pathogenic variants
QA0.0Neurodevelopmental disorders related to pathogenic variants in specific genes
QA0.01Neurodevelopmental disorders related to pathogenic variants in certain specific genes

Inclusion Terms

Official

ICD-10-CM does not list inclusion terms for QA0.01 in this effective period.

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for QA0.01 in this effective period.

Related Child Codes

Official
QA0.010Neurodevelopmental disorders, related to pathogenic variants in ion channel genes
QA0.011Neurodevelopmental disorders, related to pathogenic variants in glutamate receptor genes
QA0.012Neurodevelopmental disorders, related to pathogenic variants in other receptor genes
QA0.013Neurodevelopmental disorders, related to pathogenic variants in other transporter and solute carrier genes
QA0.014Neurodevelopmental disorders, related to pathogenic variants in synapse related genes

Includes

Official

ICD-10-CM does not list Includes notes for QA0.01 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for QA0.01 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for QA0.01 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for QA0.01 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for QA0.01 in this effective period.

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Coder workflow notes

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What This Code Means

QA0.01 is the ICD-10-CM diagnosis code for neurodevelopmental disorders related to pathogenic variants in certain specific genes. QA0.01 sits in the ICD-10-CM chapter for congenital malformations, deformations and chromosomal abnormalities (q00-qa0), within the section covering genetic disorders, not elsewhere classified (qa0).

Header codes like QA0.01 cannot be reported on claims directly, they organize child codes that share clinical context but the actual diagnosis must be coded to the highest level of specificity supported by the documentation. Coders should look at QA0.01's child codes and select the one that matches the patient's documented presentation, since payers reject header codes submitted as the primary diagnosis. For risk adjustment workflows, header codes never contribute to a Medicare Advantage member's RAF score on their own; only billable child codes that happen to map to a payment HCC affect risk-adjusted plan payments.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for QA0.01 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Child Codes

Code Hierarchy

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