D68.61
BillableAntiphospholipid syndrome
HCC Category Mapping
V24HCC 48 — Coagulation Defects and Other Specified Hematological Disorders
0.209ESRDHCC 48 — Coagulation Defects and Other Specified Hematological Disorders
0.000What This Code Means
An autoimmune condition where the body produces antibodies that interfere with blood clotting, causing either excessive bleeding or clotting.
Coding Tips
- •Document positive antiphospholipid antibody test results (anticardiolipin, anti-beta-2 glycoprotein, lupus anticoagulant)
- •Link to associated thrombotic or hemorrhagic events; this condition often coexists with lupus (SLE)
Clinical Significance
Antiphospholipid syndrome is an acquired systemic autoimmune thrombophilia characterized by vascular thrombosis (arterial or venous) and/or pregnancy morbidity in the presence of persistent antiphospholipid antibodies. It may be primary or secondary to systemic lupus erythematosus. Catastrophic antiphospholipid syndrome, involving multi-organ thrombosis, carries high mortality.
Documentation Requirements
- ✓Document positive antiphospholipid antibodies on two occasions at least 12 weeks apart (anticardiolipin IgG/IgM, anti-beta2 glycoprotein I IgG/IgM, or lupus anticoagulant), clinical criteria met (vascular thrombosis or pregnancy morbidity), and whether the condition is primary or secondary.
- ✓Record current anticoagulation regimen and target INR.
Excludes 1 — Do NOT code together
- anti-phospholipid antibody, finding without diagnosis (R76.0)
Excludes 2 — Not included here, may code separately
Commonly Confused Codes
Code Hierarchy
└D68Other coagulation defects└D68.6Other thrombophilia└D68.61Antiphospholipid syndrome
└D68.61Antiphospholipid syndrome