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D67 ICD-10-CM Code: Hereditary factor IX deficiency

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FY 2026 Apr update / Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) / Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)

D67

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Hereditary factor IX deficiency

A hereditary bleeding disorder caused by deficiency or dysfunction of clotting factor IX, commonly known as hemophilia B or Christmas disease.

Buddy the Bee presenting code insight

Buddy Insight

Hereditary factor IX deficiency (Hemophilia B, also called Christmas disease) is an X-linked recessive bleeding disorder accounting for approximately 15-20% of hemophilia cases.

CMS-HCC V28

HCC 111

RAF 4.639

CMS-HCC V24

HCC 46

RAF 1.372

ACA/HHS

N/A

Not mapped

ESRD/PACE

HCC 46

RAF 0.223

RXHCC

N/A

Not mapped

Code Book Path

Official
D6Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
D67Hereditary factor IX deficiency

Inclusion Terms

Official
  • Christmas disease
  • Factor IX deficiency (with functional defect)
  • Hemophilia B
  • Plasma thromboplastin component [PTC] deficiency

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for D67 in this effective period.

Related Child Codes

Official

ICD-10-CM does not list child codes under D67 for this display context.

Includes

Official

ICD-10-CM does not list Includes notes for D67 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for D67 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for D67 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for D67 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for D67 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance
Document factor IX activity levels and severity classification (severe, moderate, mild).
Record the specific factor IX replacement product used, dosing schedule, and any history of inhibitor development.
Note significant bleeding episodes, joint damage assessment, and current prophylaxis versus on-demand treatment strategy.

MEAT Support

HCC Buddy guidance
Document factor IX activity levels and severity classification (severe, moderate, mild).
Record the specific factor IX replacement product used, dosing schedule, and any history of inhibitor development.
Note significant bleeding episodes, joint damage assessment, and current prophylaxis versus on-demand treatment strategy.

Audit Caution

HCC Buddy guidance
Hemophilia B is commonly confused with Hemophilia A in documentation — verify the specific factor deficiency documented by the provider.
Do not assign D67 for acquired factor IX inhibitors.
Female carriers may have mildly reduced factor IX levels but typically do not warrant this diagnosis unless symptomatic.

Common Mistakes

HCC Buddy guidance
D66 (Hereditary factor VIII deficiency/Hemophilia A) — same clinical presentation but different factor deficiency
D68.1 (Hereditary factor XI deficiency) — typically milder bleeding disorder with different inheritance pattern (autosomal)
D68.2 (Hereditary deficiency of other clotting factors) — captures rarer factor deficiencies.

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Is D67 an HCC code?

Yes. D67 maps to Hemophilia, Male under the CMS-HCC V28 risk adjustment model (and Severe Hematological Disorders under V24).

HCC Category Mapping

V28HCC 111, Hemophilia, Male
4.639
V24HCC 46, Severe Hematological Disorders
1.372
ESRDHCC 46, Severe Hematological Disorders
0.223

Each model's RAF is its CMS base weight for that model's standard population, so weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member segment, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains in use during the transition and for historical data.

Work D67 in the Code Book — tabular path, V28 RAF, and MEAT checklist →

MEAT Criteria for D67

For D67to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.

  • MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
  • EEvaluate: test results, medication response, or physical findings reviewed by the provider
  • AAssess: explicit mention in the assessment or plan with acknowledgment of status
  • TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed D67 during that encounter, not just copy-forwarded from a problem list.

Coder workflow notes

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What This Code Means

D67 is the ICD-10-CM diagnosis code for hereditary factor ix deficiency. A hereditary bleeding disorder caused by deficiency or dysfunction of clotting factor IX, commonly known as hemophilia B or Christmas disease. D67 sits in the ICD-10-CM chapter for diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (d50-d89), within the section covering coagulation defects, purpura and other hemorrhagic conditions (d65-d69).

Under the CMS-HCC V28 risk adjustment model, D67 maps to Hemophilia, Male (HCC 111) with a community, non-dual, aged base RAF weight of 4.639. Under the older CMS-HCC V24 model, D67 maps to Severe Hematological Disorders (HCC 46) with a community, non-dual, aged base RAF weight of 1.372. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition.

Document the severity of the deficiency when available. Because D67 maps to a payment HCC, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's Medicare Advantage risk adjustment score. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for D67 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • Document the severity of the deficiency when available
  • Code any associated complications or inhibitor development separately

Clinical Significance

Hereditary factor IX deficiency (Hemophilia B, also called Christmas disease) is an X-linked recessive bleeding disorder accounting for approximately 15-20% of hemophilia cases. Like Hemophilia A, severity is classified by factor activity levels. Treatment involves factor IX replacement products, and gene therapy has emerged as a potential option.

Documentation Requirements

  • Document factor IX activity levels and severity classification (severe, moderate, mild).
  • Record the specific factor IX replacement product used, dosing schedule, and any history of inhibitor development.
  • Note significant bleeding episodes, joint damage assessment, and current prophylaxis versus on-demand treatment strategy.

Commonly Confused Codes

  • D66 (Hereditary factor VIII deficiency/Hemophilia A): same clinical presentation but different factor deficiency
  • D68.1 (Hereditary factor XI deficiency): typically milder bleeding disorder with different inheritance pattern (autosomal)
  • D68.2 (Hereditary deficiency of other clotting factors): captures rarer factor deficiencies.

Code Hierarchy

D67Hereditary factor IX deficiency
D67Hereditary factor IX deficiency

Because D67 maps to a payment HCC, the documentation must also satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's risk adjustment score.

D67 maps to CMS-HCC V28 category 111, Hemophilia, Male. See the ICD-10 to HCC mapping hub for how the V28 crosswalk works.

Work D67 in HCC Buddy

Open D67 in the Code Book for the full Index-to-Tabular path, MEAT checklist, and V28 HCC mapping, or in the Encoder to code from a keyword search. Pro includes 14 days to try everything.