D68.2

HCC Category Mapping

What This Code Means

An inherited bleeding disorder caused by deficiency of clotting factors other than factor VIII or IX (such as factors II, V, VII, X, XI, XII, or XIII).

Coding Tips

• •Identify which specific clotting factor is deficient in the documentation to ensure accurate coding
• •If a more specific code exists for the particular factor deficiency, use that instead of this general code

Clinical Significance

This code captures hereditary deficiencies of clotting factors other than VIII, IX, and XI, including rare conditions such as factor II (prothrombin), factor V, factor VII, factor X, factor XII, and factor XIII deficiencies. These are extremely rare autosomal recessive disorders, each with distinct bleeding phenotypes. Factor XII deficiency notably does not cause clinical bleeding despite prolonging the PTT.

Documentation Requirements

• ✓Document the specific clotting factor that is deficient, the measured factor activity level, and whether the deficiency is homozygous or heterozygous.
• ✓Record bleeding history, family history consistent with autosomal recessive inheritance, and treatment used for bleeding episodes or prophylaxis.

Commonly Confused Codes