M31.30

Billable

Wegener's granulomatosis without renal involvement

HCC Category Mapping

V28HCC 93 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.175

V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.307

ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.000

RxHCCHCC 84 — Vasculitis and Other Autoimmune Disorders

0.000

What This Code Means

A serious autoimmune disease that causes inflammation of blood vessels and granulomas (nodular growths) in the lungs and upper respiratory tract, without kidney involvement.

Coding Tips

•Confirm absence of renal involvement before using this code; if kidneys are affected, use M31.31
•Document affected organ systems (respiratory, sinuses, etc.)

Clinical Significance

Wegener's granulomatosis (now called Granulomatosis with Polyangiitis) without renal involvement represents a serious systemic necrotizing vasculitis affecting the upper and lower respiratory tract. Early treatment with immunosuppressive agents is crucial to prevent organ damage and preserve function.

Documentation Requirements

✓Clinical evidence of upper and/or lower respiratory tract involvement
✓Biopsy showing necrotizing granulomatous inflammation
✓ANCA testing results (typically c-ANCA/PR3 positive)
✓Documentation of absence of renal involvement
✓Assessment of systemic manifestations
✓Treatment response monitoring
✓Regular monitoring for renal development
✓Multisystem organ assessment

Commonly Confused Codes

M31.31 — Wegener's granulomatosis with renal involvement (when kidneys are affected)M31.7 — Microscopic polyangiitis (different ANCA-associated vasculitis)J44.1 — Chronic obstructive pulmonary disease with acute exacerbation (respiratory symptoms only)M31.2 — Lethal midline granuloma (different granulomatous condition)M35.3 — Polymyalgia rheumatica (different inflammatory condition)

Code Hierarchy

└M31Other necrotizing vasculopathies └M31.3Wegener's granulomatosis └M31.30Wegener's granulomatosis without renal involvement

└M31.30Wegener's granulomatosis without renal involvement