M31.31
BillableWegener's granulomatosis with renal involvement
HCC Category Mapping
V28HCC 93 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.175V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.307ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000RxHCCHCC 84 — Vasculitis and Other Autoimmune Disorders
0.000What This Code Means
A serious autoimmune disease that causes inflammation of blood vessels and granulomas in the lungs, upper respiratory tract, and kidneys.
Coding Tips
- •Always document the degree of renal involvement and any renal function impairment
- •Link to appropriate codes for kidney disease if present
Clinical Significance
Wegener's granulomatosis with renal involvement represents the most severe form of this systemic necrotizing vasculitis, with significant risk of kidney failure and other organ damage. The renal component indicates more extensive disease requiring aggressive immunosuppressive therapy and close monitoring.
Documentation Requirements
- ✓Clinical evidence of respiratory tract involvement
- ✓Documentation of renal involvement (hematuria, proteinuria, decreased GFR)
- ✓Biopsy evidence from affected organs
- ✓ANCA testing results
- ✓Assessment of extent of renal damage
- ✓Monitoring of kidney function over time
- ✓Treatment response in multiple organ systems
- ✓Coordination with nephrology services
Commonly Confused Codes
M31.30 — Wegener's granulomatosis without renal involvement (when kidneys not affected)M31.7 — Microscopic polyangiitis (different ANCA-associated vasculitis)N05.9 — Unspecified nephritic syndrome (isolated renal disease)J44.0 — Chronic obstructive pulmonary disease with acute lower respiratory infectionM30.0 — Polyarteritis nodosa (different systemic vasculitis)
Code Hierarchy
└M31Other necrotizing vasculopathies└M31.3Wegener's granulomatosis└M31.31Wegener's granulomatosis with renal involvement
└M31.31Wegener's granulomatosis with renal involvement