J84.89

Billable

Other specified interstitial pulmonary diseases

HCC Category Mapping

V28HCC 280 — Chronic Obstructive Pulmonary Disease

0.334

V24HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders

0.268

ESRDHCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders

0.000

RxHCCHCC 227 — Sarcoidosis, Pulmonary Alveolar Disorders

0.000

What This Code Means

Other rare lung diseases involving inflammation or scarring of the lung tissue that don't fit into more specific categories.

Coding Tips

•Use this code only when a more specific interstitial lung disease code is not available
•Document the specific diagnosis in the medical record to support appropriate code selection

Clinical Significance

Other specified interstitial pulmonary diseases captures ILDs that have been specifically identified but do not have their own dedicated ICD-10-CM code. This includes conditions such as pleuroparenchymal fibroelastosis, airway-centered interstitial fibrosis, and other rare but documented ILD entities. Proper use requires that the specific condition is documented but simply lacks a unique code.

Documentation Requirements

✓Documentation of the specific interstitial pulmonary disease by name in the medical record
✓Imaging and/or biopsy findings supporting the specific diagnosis
✓Explanation of why more specific codes (J84.1, J84.2, J84.8x) do not apply
✓Pulmonary function tests documenting disease severity
✓Treatment plan appropriate to the documented specific interstitial disease

Excludes 1 — Do NOT code together

cryptogenic organizing pneumonia (J84.116)
idiopathic non-specific interstitial pneumonitis (J84.113)
lipoid pneumonia, exogenous or unspecified (J69.1)
lymphoid interstitial pneumonia (J84.2)

Use Additional Code

code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced

Code First

, if applicable:
poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
underlying cause of pneumonopathy, if known

Commonly Confused Codes

J84.9 — Interstitial pulmonary disease unspecified is for when the type of ILD is NOT known; J84.89 is for known but non-codeable types J84.111 — Idiopathic interstitial pneumonia NOS should be used when the IIP subtype is unidentified within the IIP classification J84.112 — Idiopathic pulmonary fibrosis has its own specific code and should never be coded as J84.89 J84.10 — Pulmonary fibrosis unspecified is a different category for fibrotic disease without specification

Code Hierarchy

└J84Other interstitial pulmonary diseases └J84.8Other specified interstitial pulmonary diseases └J84.89Other specified interstitial pulmonary diseases

└J84.89Other specified interstitial pulmonary diseases