J84.2
BillableLymphoid interstitial pneumonia
HCC Category Mapping
V28HCC 280 — Chronic Obstructive Pulmonary Disease
0.334V24HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
0.268ESRDHCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
0.000RxHCCHCC 227 — Sarcoidosis, Pulmonary Alveolar Disorders
0.000What This Code Means
A lung disease where immune cells accumulate in the tissue between air sacs, causing inflammation and breathing difficulties.
Coding Tips
- •Confirm lymphoid infiltration on biopsy or imaging to differentiate from other interstitial pneumonias
- •Document any associated autoimmune conditions that may be present
Clinical Significance
Lymphoid interstitial pneumonia is a rare lymphoproliferative disorder of the lung characterized by diffuse lymphocytic infiltration of the pulmonary interstitium. It is frequently associated with autoimmune conditions (particularly Sjogren syndrome) and immunodeficiency states including HIV. Accurate coding reflects the complex multisystem management these patients require.
Documentation Requirements
- ✓Lung biopsy confirming lymphoid interstitial pneumonia pattern with diffuse lymphocytic infiltration
- ✓High-resolution computed tomography findings (ground-glass opacities, thin-walled cysts, centrilobular nodules)
- ✓Documentation of associated conditions (Sjogren syndrome, HIV, other autoimmune diseases, immunodeficiency)
- ✓Exclusion of lymphoma and other lymphoproliferative malignancies
- ✓Treatment plan and monitoring for potential transformation to lymphoma
Commonly Confused Codes
C85.9 — Non-Hodgkin lymphoma unspecified must be excluded, as LIP can transform to lymphomaJ84.111 — Idiopathic interstitial pneumonia NOS does not capture the specific lymphoid patternJ84.89 — Other specified interstitial pulmonary diseases is less specific than the dedicated LIP codeD47.Z2 — Follicular dendritic cell sarcoma is a lymphoproliferative disorder but malignant, unlike LIP
Code Hierarchy
└J84Other interstitial pulmonary diseases└J84.2Lymphoid interstitial pneumonia
└J84.2Lymphoid interstitial pneumonia