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I77.82

Billable

Antineutrophilic cytoplasmic antibody [ANCA] vasculitis

HCC Category Mapping

V28HCC 93Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.175
V24HCC 40Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.307
ESRDHCC 40Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000
RxHCCHCC 83Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000

What This Code Means

This is an autoimmune disease where the body's immune system attacks blood vessels, causing inflammation and damage to multiple organs. It is identified by the presence of specific antibodies (ANCA) in the blood that target neutrophil proteins.

Coding Tips

  • Verify the specific type of ANCA vasculitis (such as granulomatosis with polyangiitis, microscopic polyangiitis, or eosinophilic granulomatosis with polyangiitis) in the documentation, as more specific codes may be available
  • Document which organs are affected (lungs, kidneys, skin, etc.) as this information may support medical necessity and justify treatment decisions

Clinical Significance

Antineutrophilic cytoplasmic antibody vasculitis is a systemic autoimmune condition causing inflammation and destruction of small blood vessels, potentially affecting kidneys, lungs, skin, and nerves. This is a serious condition requiring immunosuppressive therapy and carrying significant morbidity. It maps to multiple HCC categories across models, reflecting its multi-system impact and high clinical complexity.

Documentation Requirements

  • Positive antineutrophilic cytoplasmic antibody serology with pattern specification (cytoplasmic or perinuclear)
  • Specific antineutrophilic cytoplasmic antibody-associated diagnosis: granulomatosis with polyangiitis, microscopic polyangiitis, or eosinophilic granulomatosis with polyangiitis
  • Organ involvement documentation (renal, pulmonary, dermatologic, neurologic)
  • Biopsy results when available showing vasculitis or glomerulonephritis
  • Current immunosuppressive treatment regimen
  • Disease activity status — active flare, remission, or maintenance
  • Monitoring labs including renal function, urinalysis, and inflammatory markers

Excludes 2 — Not included here, may code separately

  • eosinophilic granulomatosis with polyangiitis (M30.1)
  • granulomatosis with polyangiitis (M31.3-)
  • microscopic polyangiitis (M31.7)

Commonly Confused Codes

Code Hierarchy

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