M30.1
BillablePolyarteritis with lung involvement [Churg-Strauss]
HCC Category Mapping
V28HCC 278 — Fibrosis of Lung and Other Chronic Lung Disorders
1.091V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.307ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000RxHCCHCC 84 — Vasculitis and Other Autoimmune Disorders
0.000What This Code Means
A rare inflammatory disease (Churg-Strauss syndrome) that affects blood vessels and causes inflammation in the lungs along with other systemic symptoms.
Coding Tips
- •This condition is also known as eosinophilic granulomatosis with polyangiitis (EGPA); document the preferred terminology used
- •Specify the extent of lung involvement and any other affected organs for complete clinical picture
Clinical Significance
Churg-Strauss syndrome (Eosinophilic Granulomatosis with Polyangiitis) is a rare, life-threatening systemic vasculitis with prominent lung involvement and eosinophilia. The condition requires immediate aggressive treatment and has a high risk of organ damage and mortality if untreated.
Documentation Requirements
- ✓Clinical triad of asthma, eosinophilia, and systemic vasculitis
- ✓Pulmonary involvement documentation
- ✓Biopsy showing eosinophilic infiltration and necrotizing vasculitis
- ✓Laboratory evidence of eosinophilia
- ✓ANCA testing results if available
- ✓Documentation of affected organ systems
- ✓Assessment of cardiac involvement
- ✓Treatment response monitoring
Commonly Confused Codes
M30.0 — Polyarteritis nodosa (without lung involvement)J45.9 — Asthma, unspecified (when only respiratory symptoms are coded)M31.30 — Wegener's granulomatosis without renal involvementD72.1 — Eosinophilia (when only blood abnormality is coded)M35.9 — Systemic involvement of connective tissue, unspecified
Code Hierarchy
└M30Polyarteritis nodosa and related conditions└M30.1Polyarteritis with lung involvement [Churg-Strauss]
└M30.1Polyarteritis with lung involvement [Churg-Strauss]