E80.5
BillableCrigler-Najjar syndrome
This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).
What This Code Means
A rare inherited disorder where the liver cannot properly process bilirubin, leading to severe jaundice in newborns and potential brain damage if untreated.
Coding Tips
- •Specify Type I or Type II Crigler-Najjar syndrome when documented, as they have different severity levels
- •Often requires phototherapy or exchange transfusion in neonates; coordinate coding with newborn complications
Code Hierarchy
└E80Disorders of porphyrin and bilirubin metabolism└E80.5Crigler-Najjar syndrome
└E80.5Crigler-Najjar syndrome