E75.5
BillableOther lipid storage disorders
HCC Category Mapping
RxHCCHCC 43 — Other Significant Endocrine and Metabolic Disorders
0.000What This Code Means
A category for rare inherited metabolic disorders involving abnormal accumulation of lipids in the body that do not fit into other specific lipid storage disease categories.
Coding Tips
- •Use this code for lipid storage disorders not classified elsewhere
- •Ensure documentation specifies the type of lipid involved and affected organ systems
Clinical Significance
Other lipid storage disorders capture rare inherited conditions where lipids accumulate abnormally in cells but do not fall into the specific sphingolipidosis or ceroid lipofuscinosis categories. These conditions cause progressive organ damage and require complex, long-term management with significant healthcare resource consumption.
Documentation Requirements
- ✓Specific lipid storage disorder type documented (e.g., Wolman disease, cholesteryl ester storage disease, acid lipase deficiency)
- ✓Confirmatory diagnostic testing (enzyme assay, genetic testing, or tissue biopsy)
- ✓Affected organ systems and current clinical manifestations
- ✓Treatment plan including any enzyme replacement or dietary management
- ✓Provider assessment confirming this is a storage disorder, not a simple lipid metabolism issue
Commonly Confused Codes
E75.21-E75.29 — Sphingolipidoses: use when the lipid storage disorder specifically involves sphingolipidsE75.4 — Neuronal ceroid lipofuscinosis: a specific type with its own code, not 'other'E75.6 — Lipid storage disorder, unspecified: use only when the type cannot be determinedE78.89 — Other lipoprotein metabolism disorders: for lipoprotein processing errors, not intracellular storageE78.70 — Disorder of bile acid and cholesterol metabolism, unspecified: for cholesterol metabolism pathway issues, not storage
Code Hierarchy
└E75Disorders of sphingolipid metabolism and other lipid storage disorders└E75.5Other lipid storage disorders
└E75.5Other lipid storage disorders