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D71.1 ICD-10-CM Code: Leukocyte adhesion deficiency

ICD-10-CM Code View

HCC Buddy Code Card

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FY 2026 Apr update / Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) / Other disorders of blood and blood-forming organs (D70-D77)

D71.1

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Leukocyte adhesion deficiency

A rare inherited disorder where white blood cells cannot properly stick to blood vessel walls and tissues to fight infections.

CMS-HCC V28

HCC 115

RAF 0.565

CMS-HCC V24

N/A

Not mapped

ACA/HHS

HCC 74

Varies by metal level

ESRD/PACE

HCC 47

RAF 0.078

RXHCC

N/A

Not mapped

Code Book Path

Official
D71Functional disorders of polymorphonuclear neutrophils
D71.1Leukocyte adhesion deficiency

Inclusion Terms

Official
  • LAD-I
  • LAD-II
  • LAD-III
  • Leukocyte adhesion deficiency type I
  • Leukocyte adhesion deficiency type II

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for D71.1 in this effective period.

Related Child Codes

Official
D71.8Other functional disorders of polymorphonuclear neutrophils
D71.9Functional disorders of polymorphonuclear neutrophils, unspecified

Includes

Official

ICD-10-CM does not list Includes notes for D71.1 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for D71.1 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for D71.1 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for D71.1 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for D71.1 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance
This is a congenital immunodeficiency; document the genetic nature and family history when available
Verify the specific adhesion molecule defect is documented if possible (CD11/CD18 deficiency)

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Is D71.1 an HCC code?

Yes. D71.1 (Leukocyte adhesion deficiency) maps to Specified Immunodeficiencies and White Blood Cell Disorders under the CMS-HCC V28 risk adjustment model, with a community non-dual aged RAF of 0.565. It is billable for payment year 2026.

Coder answer: D71.1 is billable and maps to V28 HCC 115, Specified Immunodeficiencies and White Blood Cell Disorders. Open it in the Code Book for the tabular path, RAF, and MEAT checklist.

Code
D71.1
Description
Leukocyte adhesion deficiency
HCC (V28)
HCC 115 — Specified Immunodeficiencies and White Blood Cell Disorders
RAF
0.565
Billable
Yes
Payment year
2026

HCC Category Mapping

V28HCC 115, Specified Immunodeficiencies and White Blood Cell Disorders
0.565
ESRDHCC 47, Disorders of Immunity
0.078

Each model's RAF is its CMS base weight for that model's standard population, so weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member segment, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains in use during the transition and for historical data.

Work D71.1 in the Code Book — tabular path, V28 RAF, and MEAT checklist →

MEAT Criteria for D71.1

For D71.1 to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.

  • MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
  • EEvaluate: test results, medication response, or physical findings reviewed by the provider
  • AAssess: explicit mention in the assessment or plan with acknowledgment of status
  • TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed D71.1 during that encounter, not just copy-forwarded from a problem list.

Coder workflow notes

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What This Code Means

D71.1 is the ICD-10-CM diagnosis code for leukocyte adhesion deficiency. A rare inherited disorder where white blood cells cannot properly stick to blood vessel walls and tissues to fight infections. D71.1 sits in the ICD-10-CM chapter for diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (d50-d89), within the section covering other disorders of blood and blood-forming organs (d70-d77).

Under the CMS-HCC V28 risk adjustment model, D71.1 maps to Specified Immunodeficiencies and White Blood Cell Disorders (HCC 115) with a community, non-dual, aged base RAF weight of 0.565. D71.1 was not retained as a payment HCC under the older V24 model, so V28 introduced or recategorized it during the 2024–2026 phase-in. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition.

This is a congenital immunodeficiency; document the genetic nature and family history when available. Because D71.1 maps to a payment HCC, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's Medicare Advantage risk adjustment score. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for D71.1 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • This is a congenital immunodeficiency; document the genetic nature and family history when available
  • Verify the specific adhesion molecule defect is documented if possible (CD11/CD18 deficiency)

Child Codes

Code Hierarchy

D71.1 code history

Code setChange
FY2026 (effective Oct 1, 2025)Added to the code set

Source: official CMS ICD-10-CM order and addenda files, FY2016 through FY2027.

Because D71.1 maps to a payment HCC, the documentation must also satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's risk adjustment score.

D71.1 maps to CMS-HCC V28 category 115, Specified Immunodeficiencies and White Blood Cell Disorders. See the ICD-10 to HCC mapping hub for how the V28 crosswalk works. Because D71.1 carries a payment HCC, you can see what it adds to a RAF score and check the documentation the chart needs before it is submitted.

Work D71.1 in HCC Buddy

Open D71.1 in the Code Book for the full Index-to-Tabular path, MEAT checklist, and V28 HCC mapping, or in the Encoder to code from a keyword search. Pro includes 7 days to try everything, no card required.