D57.814

HCC Category Mapping

What This Code Means

A rare sickle-cell disorder with dactylitis, which is severe pain and swelling in the hands and feet.

Coding Tips

• •Dactylitis is often one of the first manifestations of sickle-cell disease in children; verify documentation of hand/foot involvement
• •Ensure the swelling and pain are specifically attributed to sickle-cell disease rather than other causes

Clinical Significance

Other sickle-cell disorders with dactylitis describes painful vaso-occlusive crises affecting the small bones of the hands and feet in patients with rare sickle-cell variants. Dactylitis (hand-foot syndrome) is often the earliest clinical manifestation of sickle-cell disease in infants and young children, typically presenting between 6 months and 2 years of age. The condition causes symmetric painful swelling of the digits and can lead to permanent bone damage if recurrent.

Documentation Requirements

• ✓Document the specific sickle-cell variant and clinical findings of hand and/or foot swelling with pain.
• ✓Include radiographic findings if obtained, showing soft tissue swelling or periosteal reaction.
• ✓Record patient age at presentation, symptom duration, and response to treatment.
• ✓Document any prior episodes of dactylitis and evidence of bone changes from recurrent episodes.

Commonly Confused Codes