D57.218

HCC Category Mapping

What This Code Means

A blood disorder combining sickle cell disease and hemoglobin C disease with a sudden crisis episode involving complications other than those specifically listed.

Coding Tips

• •Use this code when documentation describes a specific complication not captured by D57.211-214; clearly document what the complication is
• •Ensure the complication is acute and crisis-related, not a chronic manifestation

Clinical Significance

This code captures sickle-cell/Hemoglobin C disease crises with specified complications not classified under acute chest syndrome, splenic sequestration, cerebral vascular involvement, or dactylitis. Hemoglobin SC-specific complications may include proliferative retinopathy crisis, avascular necrosis exacerbation, priapism, hepatic sequestration, or renal complications. Hemoglobin SC patients are particularly prone to retinal and orthopedic complications compared to other sickle cell genotypes.

Documentation Requirements

• ✓Documentation must confirm the Hemoglobin SC genotype and identify the specific crisis complication.
• ✓The provider should describe the complication type, clinical presentation, supporting diagnostic findings, treatment administered, and clinical outcome.
• ✓Record whether the complication results in permanent organ damage.
• ✓Specify why the complication does not fit into the D57.211-D57.214 categories.

Commonly Confused Codes