C86.50

HCC Category Mapping

What This Code Means

A rare lymphoma caused by abnormal T-cells that affects lymph nodes and surrounding tissues and has not achieved remission.

Coding Tips

• •Confirm active disease status and lack of remission
• •Distinguish from C86.51 which indicates remission status

Clinical Significance

Angioimmunoblastic T-cell lymphoma (AITL) is a systemic, typically aggressive mature T-cell neoplasm characterized by generalized lymphadenopathy, hepatosplenomegaly, skin rash, and prominent systemic symptoms including fever, weight loss, and night sweats. It is commonly associated with autoimmune phenomena including hypergammaglobulinemia, positive Coombs test, and circulating immune complexes. Non-remission status indicates ongoing active disease despite treatment efforts.

Documentation Requirements

• ✓Documentation must confirm AITL through lymph node biopsy with characteristic pathology (proliferation of follicular dendritic cells, high endothelial venules, and T-follicular helper cell markers).
• ✓Associated autoimmune manifestations, staging workup, treatment regimen, and explicit non-remission status must be documented.

Commonly Confused Codes