Q99.818
BillableOther Usher syndrome
This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).
What This Code Means
A genetic disorder causing progressive hearing loss and vision loss (retinitis pigmentosa) that does not fit the typical patterns of types 1, 2, or 3 Usher syndrome.
Coding Tips
- •Use this code only when Usher syndrome is confirmed but does not meet criteria for types 1, 2, or 3
- •Document the specific clinical features and genetic findings that support the Usher syndrome diagnosis