Q89.81
BillableKabuki syndrome
This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).
What This Code Means
A rare genetic disorder present from birth characterized by distinctive facial features, developmental delays, and various organ abnormalities.
Coding Tips
- •Kabuki syndrome is a specific recognizable pattern; do not use Q89.7 if Kabuki is confirmed
- •Code associated complications such as cardiac defects or intellectual disability separately