Q85.00

Billable

Neurofibromatosis, unspecified

HCC Category Mapping

V28HCC 23 — Melanoma and Other Skin Cancers

0.251

V24HCC 12 — Breast, Prostate, and Other Cancers and Tumors

0.150

ESRDHCC 12 — Breast, Prostate, and Other Cancers and Tumors

0.000

What This Code Means

A genetic disorder causing multiple benign tumors to grow along nerves throughout the body, type not specified.

Coding Tips

•Verify whether the patient has NF1 or NF2 before using this unspecified code
•Document any complications or manifestations (optic nerve gliomas, neurofibromas, etc.) separately

Clinical Significance

Unspecified neurofibromatosis represents a significant genetic tumor predisposition syndrome requiring lifelong monitoring for malignant transformation and complications. The condition affects multiple organ systems and has cancer risk implications, making accurate diagnosis and regular surveillance essential for optimal patient outcomes and early intervention.

Documentation Requirements

✓Clinical evidence of multiple neurofibromas
✓Family history of neurofibromatosis
✓Reason why specific NF type cannot be determined
✓Associated manifestations (café-au-lait spots, etc.)
✓Neurological complications if present
✓Genetic counseling documentation
✓Screening for malignant transformation

Commonly Confused Codes

Q85.01 — NF1 when von Recklinghausen criteria are met Q85.02 — NF2 when bilateral acoustic neuromas present Q85.03 — Schwannomatosis when multiple schwannomas documented D36.10 — Benign neoplasm of peripheral nerves (individual tumor, not syndrome)

Code Hierarchy

└Q85Phakomatoses, not elsewhere classified └Q85.0Neurofibromatosis (nonmalignant)└Q85.00Neurofibromatosis, unspecified

└Q85.00Neurofibromatosis, unspecified