Q79.61

Billable

Classical Ehlers-Danlos syndrome

HCC Category Mapping

RxHCCHCC 84 — Vasculitis and Other Autoimmune Disorders

0.000

What This Code Means

A genetic disorder affecting connective tissue that causes joint hypermobility, skin fragility, and tissue weakness, with characteristic features including velvety skin and easy bruising.

Coding Tips

•Verify documentation specifies 'classical' type to distinguish from other EDS subtypes
•Look for associated complications like joint dislocations or vascular issues that may require additional coding

Clinical Significance

Classical Ehlers-Danlos syndrome is a well-defined connective tissue disorder with characteristic skin hyperextensibility, joint hypermobility, and tissue fragility requiring specialized care to prevent complications. Patients need careful monitoring for wound healing issues and joint injuries, with specific management protocols for surgeries and dental procedures.

Documentation Requirements

✓Documentation of major criteria (skin hyperextensibility, atrophic scarring, joint hypermobility)
✓Minor criteria present (smooth, velvety skin, easy bruising, etc.)
✓Family history of classical EDS
✓Genetic testing confirming COL5A1 or COL5A2 mutations
✓Exclusion of vascular EDS type
✓Joint hypermobility score documentation
✓Assessment of functional limitations

Commonly Confused Codes

Q79.60 — Unspecified EDS when classical type is documented Q79.62 — Hypermobile EDS (less severe skin involvement)Q79.63 — Vascular EDS (more serious with vessel fragility)M35.9 — Connective tissue disorder without specific EDS diagnosis

Code Hierarchy

└Q79Congenital malformations of musculoskeletal system, not elsewhere classified └Q79.6Ehlers-Danlos syndromes └Q79.61Classical Ehlers-Danlos syndrome

└Q79.61Classical Ehlers-Danlos syndrome