Q56.2
BillableFemale pseudohermaphroditism, not elsewhere classified
This code does not map to an HCC category in any model (V28, V24, ESRD, RxHCC).
What This Code Means
A birth condition where a person with female chromosomes and ovaries has external genitalia that appear male or ambiguous.
Coding Tips
- •Often associated with congenital adrenal hyperplasia; review documentation for underlying endocrine conditions
- •Distinguish from male pseudohermaphroditism (Q56.1) which involves male chromosomes with feminized features
Code Hierarchy
└Q56Indeterminate sex and pseudohermaphroditism└Q56.2Female pseudohermaphroditism, not elsewhere classified
└Q56.2Female pseudohermaphroditism, not elsewhere classified