FY2027 ICD-10-CM reference
Q43.1: Hirschsprung's disease
By the HCC Buddy Coding Team
The official ICD-10-CM descriptor is Hirschsprung's disease. The FY2027 annual edition starts October 1, 2026. Check the edition that applies to the encounter or inpatient discharge, including any April update.
Billable code. Verified against the official FY2027 order file.
FY2027 Tabular instructions
Instructions below include applicable chapter, section and parent-code notes. Each note identifies where it appears in the official source.
Instructional note
Codes from this chapter are not for use on maternal records
Source: Q00-QA1 (chapter, inherited).
Excludes2
inborn errors of metabolism (E70-E88)
Source: Q00-QA1 (chapter, inherited).
Instructional note
Aganglionosis
Source: Q43.1 (self, direct).
Instructional note
Congenital (aganglionic) megacolon
Source: Q43.1 (self, direct).
Compare the FY2027 additions, removals and billable-status changes
What does Q43.1 mean in FY2027?
The official ICD-10-CM descriptor is Hirschsprung's disease. The FY2027 annual edition starts October 1, 2026. Check the edition that applies to the encounter or inpatient discharge, including any April update.
Is Q43.1 billable in FY2027?
The FY2027 order file marks Q43.1 as billable. Check the complete Tabular instructions and documentation before assigning it.
Does Q43.1 map to an HCC?
In the CMS 2027 Initial ICD-10-CM Mappings (payment year 2027, 2026 dates of service), Q43.1 maps to CMS-HCC V28 HCC 78 (Intestinal Obstruction/Perforation). For 2027 dates of service, CMS has not yet published the payment year 2028 mappings. ESRD, RxHCC, PACE and HHS-HCC mappings are still pending verification for FY2027.
Source: CMS FY2027 ICD-10-CM order file. Read the FY2027 Official Guidelines.
Review the FY2026 April edition