Q40.0

Billable

Congenital hypertrophic pyloric stenosis

HCC Category Mapping

V28HCC 78 — Intestinal Obstruction/Perforation

0.000

What This Code Means

A birth defect where the muscle at the outlet of the stomach becomes thickened, preventing food from passing into the small intestine and causing severe vomiting in infants.

Coding Tips

•This condition typically presents in infants 2-8 weeks old; document the age of presentation
•Note whether the diagnosis was confirmed by ultrasound or other imaging

Clinical Significance

Congenital hypertrophic pyloric stenosis is a common surgical emergency in infants that can rapidly lead to dehydration, electrolyte imbalances, and failure to thrive if not promptly diagnosed and treated. Early recognition and surgical intervention (pyloromyotomy) typically result in excellent outcomes.

Documentation Requirements

✓Clinical presentation of projectile vomiting in infant
✓Physical examination findings (palpable pyloric mass)
✓Ultrasound confirmation of pyloric muscle thickening
✓Laboratory evidence of metabolic alkalosis and dehydration
✓Age at presentation and symptom onset
✓Surgical intervention details (laparoscopic vs open pyloromyotomy)
✓Post-operative recovery and feeding tolerance
✓Follow-up outcomes and complications if any

Commonly Confused Codes

K31.1 — Adult hypertrophic pyloric stenosis (acquired condition in adults)P92.0 — Vomiting of newborn (simple vomiting without anatomic cause)Q40.1 — Congenital hiatus hernia (different anatomic abnormality)Q39.0 — Atresia of esophagus without fistula (upper GI atresia)

Code Hierarchy

└Q40Other congenital malformations of upper alimentary tract └Q40.0Congenital hypertrophic pyloric stenosis

└Q40.0Congenital hypertrophic pyloric stenosis