Q20.1

Billable

Double outlet right ventricle

HCC Category Mapping

RxHCCHCC 191 — Congenital Heart/Circulatory Disorders and Fontan Circulation

0.000

What This Code Means

A complex heart defect where both the pulmonary artery and aorta originate from the right ventricle instead of their normal positions.

Coding Tips

•Specify the relationship of the great arteries and any associated septal defects
•Document the presence of pulmonary stenosis or other hemodynamic complications

Clinical Significance

Double outlet right ventricle is a complex cyanotic congenital heart defect where both great arteries originate from the right ventricle, creating abnormal blood flow patterns. This condition typically requires multiple staged surgical interventions and lifelong cardiac monitoring for optimal outcomes.

Documentation Requirements

✓Echocardiographic confirmation of both great arteries from right ventricle
✓Position of ventricular septal defect in relation to great arteries
✓Associated cardiac anomalies
✓Degree of cyanosis and oxygen saturation
✓Surgical intervention history and type of repair
✓Current functional status and exercise tolerance
✓Arrhythmia monitoring and management
✓Ongoing cardiothoracic surgery follow-up

Commonly Confused Codes

Q20.0 — common arterial trunk Q20.2 — double outlet left ventricle Q21.3 — tetralogy of Fallot Q20.3 — discordant ventriculoarterial connection Q24.5 — malformation of coronary vessels

Code Hierarchy

└Q20Congenital malformations of cardiac chambers and connections └Q20.1Double outlet right ventricle

└Q20.1Double outlet right ventricle