Q07.01
BillableArnold-Chiari syndrome with spina bifida
HCC Category Mapping
V28HCC 182 — Spinal Cord Disorders/Injuries
0.282V24HCC 72 — Spinal Cord Disorders/Injuries
0.464ESRDHCC 72 — Spinal Cord Disorders/Injuries
0.000RxHCCHCC 155 — Myelitis and Encephalomyelitis
0.000What This Code Means
A birth defect where brain tissue extends into the spinal canal combined with an opening in the spine (spina bifida), causing neurological problems.
Coding Tips
- •Verify documentation specifies Arnold-Chiari syndrome with spina bifida only, without hydrocephalus, to distinguish from Q07.03
- •Review imaging reports and neurology notes to confirm the presence of both conditions
Clinical Significance
Arnold-Chiari syndrome with spina bifida represents a complex combination of brain herniation and open spine defects, significantly increasing morbidity and requiring intensive multidisciplinary management. This combination often necessitates multiple surgical interventions and lifelong specialized care.
Documentation Requirements
- ✓MRI confirmation of cerebellar tonsillar herniation
- ✓Documentation of concurrent spina bifida
- ✓Neurological deficits from both conditions
- ✓Surgical intervention history for both anomalies
- ✓Current functional status and disabilities
- ✓Associated complications and secondary conditions
- ✓Multidisciplinary care team involvement
- ✓Ongoing monitoring and management plans
Commonly Confused Codes
Code Hierarchy
└Q07Other congenital malformations of nervous system└Q07.0Arnold-Chiari syndrome└Q07.01Arnold-Chiari syndrome with spina bifida
└Q07.01Arnold-Chiari syndrome with spina bifida