Q03.0
BillableMalformations of aqueduct of Sylvius
HCC Category Mapping
V28HCC 182 — Spinal Cord Disorders/Injuries
0.282V24HCC 72 — Spinal Cord Disorders/Injuries
0.464ESRDHCC 72 — Spinal Cord Disorders/Injuries
0.000RxHCCHCC 155 — Myelitis and Encephalomyelitis
0.000What This Code Means
A birth defect affecting the narrow passage in the brain that allows fluid to flow, which can lead to fluid buildup and increased pressure.
Coding Tips
- •This often results in hydrocephalus; document whether hydrocephalus is present and if shunting was performed
- •Specify if the malformation is stenosis, atresia, or other type if documented
Clinical Significance
Malformations of the aqueduct of Sylvius cause obstructive hydrocephalus, leading to increased intracranial pressure and potential brain damage. This congenital condition requires lifelong monitoring and often surgical intervention with shunt placement for cerebrospinal fluid diversion.
Documentation Requirements
- ✓Documentation of congenital malformation specifically affecting aqueduct of Sylvius
- ✓Evidence of hydrocephalus or cerebrospinal fluid flow obstruction
- ✓Neurological assessment and developmental status
- ✓Neuroimaging findings confirming aqueductal abnormality
- ✓Documentation of increased intracranial pressure signs if present
- ✓Assessment of associated neurological deficits
- ✓Treatment history including shunt placement or other interventions
- ✓Ongoing monitoring requirements and complications
Commonly Confused Codes
Q03.1 — Atresia of foramina involves different CSF drainage pathwaysQ03.8 — Other congenital hydrocephalus has different anatomical causesG91.1 — Obstructive hydrocephalus may be acquired, not congenitalG93.2 — Benign intracranial hypertension is not structural malformationQ04.3 — Other brain reduction deformities don't specifically involve aqueduct
Code Hierarchy
└Q03Congenital hydrocephalus└Q03.0Malformations of aqueduct of Sylvius
└Q03.0Malformations of aqueduct of Sylvius