M35.0B

Billable

Sjögren syndrome with vasculitis

HCC Category Mapping

V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.307

ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.000

RxHCCHCC 84 — Vasculitis and Other Autoimmune Disorders

0.000

What This Code Means

Sjögren syndrome with vasculitis indicates the autoimmune condition has progressed to cause inflammation of blood vessels throughout the body.

Coding Tips

•This combination code includes both the Sjögren diagnosis and vasculitis; do not separately code vasculitis
•Document which blood vessels are affected to support medical necessity and severity assessment

Clinical Significance

Sjögren syndrome with vasculitis represents a severe systemic autoimmune complication requiring intensive immunosuppressive therapy and monitoring for organ damage. This combination significantly increases morbidity risk and healthcare resource utilization compared to uncomplicated Sjögren syndrome.

Documentation Requirements

✓Confirmed diagnosis of Sjögren syndrome with positive serology or salivary gland biopsy
✓Documentation of vasculitis with specific organs/systems affected
✓Evidence of vascular inflammation through imaging, biopsy, or clinical manifestations
✓Exclusion of other causes of vasculitis
✓Description of severity and extent of vascular involvement
✓Current treatment regimen including immunosuppressive medications
✓Assessment of functional impact on affected organs

Commonly Confused Codes

M35.00 — Sjögren syndrome, unspecified (lacks vasculitis component)M31.9 — Systemic vasculitis, unspecified (lacks Sjögren syndrome component)M35.0A — Sjögren syndrome with keratoconjunctivitis (different organ involvement)M35.0C — Sjögren syndrome with dental involvement (different complication)M32.10 — Systemic lupus erythematosus with organ involvement (different autoimmune disease)

Code Hierarchy

└M35Other systemic involvement of connective tissue └M35.0Sjögren syndrome └M35.0BSjögren syndrome with vasculitis

└M35.0BSjögren syndrome with vasculitis