M35.04
BillableSjögren syndrome with tubulo-interstitial nephropathy
HCC Category Mapping
V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.307ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000RxHCCHCC 84 — Vasculitis and Other Autoimmune Disorders
0.000What This Code Means
Sjögren syndrome affecting the kidneys, specifically the tubules and interstitium, which can impair kidney function.
Coding Tips
- •Document renal function tests and urinalysis findings to support tubulo-interstitial nephropathy diagnosis.
- •This manifestation may be asymptomatic and discovered only through laboratory abnormalities.
Clinical Significance
Sjögren syndrome with renal involvement, specifically tubulo-interstitial nephropathy, indicates serious systemic disease affecting kidney function. This manifestation requires nephrology consultation and careful monitoring of renal function and electrolyte balance.
Documentation Requirements
- ✓Confirmed diagnosis of Sjögren syndrome
- ✓Evidence of kidney dysfunction (elevated creatinine, proteinuria)
- ✓Renal biopsy showing tubulo-interstitial changes if performed
- ✓Urinalysis abnormalities consistent with tubular dysfunction
- ✓Electrolyte abnormalities (hypokalemia, renal tubular acidosis)
- ✓Nephrology consultation and recommendations
- ✓Exclusion of other causes of kidney disease
Commonly Confused Codes
M35.00 — Sjögren syndrome unspecified (use when renal involvement not documented)M35.0A — Sjögren syndrome with glomerular disease (different type of renal involvement)N15.9 — Renal tubulo-interstitial disease unspecified (use when not related to Sjögren)N18.6 — End stage renal disease (use for advanced kidney failure)
Code Hierarchy
└M35Other systemic involvement of connective tissue└M35.0Sjögren syndrome└M35.04Sjögren syndrome with tubulo-interstitial nephropathy
└M35.04Sjögren syndrome with tubulo-interstitial nephropathy