M35.02

Billable

Sjögren syndrome with lung involvement

HCC Category Mapping

V28HCC 280 — Chronic Obstructive Pulmonary Disease

0.334

What This Code Means

Sjögren syndrome with involvement of the lungs, which can cause inflammation, scarring, or breathing difficulties.

Coding Tips

•Pulmonary involvement may present as interstitial lung disease; ensure imaging or pulmonary function tests are documented.
•Code separately for any specific lung conditions (such as interstitial pneumonia) if they are documented in addition to Sjögren syndrome.

Clinical Significance

Sjögren syndrome with pulmonary involvement represents advanced systemic disease with potential for significant respiratory complications including interstitial lung disease and decreased pulmonary function. Requires pulmonology consultation and monitoring.

Documentation Requirements

✓Confirmed diagnosis of Sjögren syndrome
✓Pulmonary function test abnormalities
✓Chest imaging showing lung involvement (CT scan preferred)
✓Documentation of respiratory symptoms or complications
✓Pulmonologist evaluation and recommendations
✓Exclusion of other causes of lung disease
✓Current respiratory treatment plan

Commonly Confused Codes

M35.00 — Sjögren syndrome unspecified (use when lung involvement not documented)J84.10 — Pulmonary fibrosis unspecified (use when fibrosis not related to Sjögren)M35.03 — Sjögren syndrome with myopathy (different organ system involvement)J44.1 — COPD with acute exacerbation (different etiology)

Code Hierarchy

└M35Other systemic involvement of connective tissue └M35.0Sjögren syndrome └M35.02Sjögren syndrome with lung involvement

└M35.02Sjögren syndrome with lung involvement