M35.01

Billable

Sjögren syndrome with keratoconjunctivitis

HCC Category Mapping

V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.307

ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.000

RxHCCHCC 84 — Vasculitis and Other Autoimmune Disorders

0.000

What This Code Means

Sjögren syndrome affecting the eyes and tear glands, causing dry eyes and inflammation of the cornea and conjunctiva.

Coding Tips

•Document the presence of keratoconjunctivitis (dry eye inflammation) in the clinical notes to support this code selection.
•This is the most common organ manifestation of Sjögren syndrome and may be the presenting symptom.

Clinical Significance

This code identifies Sjögren syndrome with specific ocular involvement, indicating more severe disease requiring ophthalmologic monitoring and specialized treatment. Keratoconjunctivitis sicca can lead to corneal damage without proper management.

Documentation Requirements

✓Diagnosis of Sjögren syndrome confirmed
✓Documentation of keratoconjunctivitis or severe dry eyes
✓Schirmer test results or tear film assessment
✓Ophthalmologic examination findings
✓Corneal staining results if performed
✓Treatment response to artificial tears or other therapies
✓Any corneal complications or visual impairment

Commonly Confused Codes

M35.00 — Sjögren syndrome unspecified (use when eye involvement not specifically documented)H04.12 — Dry eye syndrome (use for isolated dry eyes without systemic Sjögren)H16.9 — Unspecified keratitis (use when keratitis not related to Sjögren)M35.02 — Sjögren syndrome with lung involvement (different organ system)

Code Hierarchy

└M35Other systemic involvement of connective tissue └M35.0Sjögren syndrome └M35.01Sjögren syndrome with keratoconjunctivitis

└M35.01Sjögren syndrome with keratoconjunctivitis