M34.82
BillableSystemic sclerosis with myopathy
HCC Category Mapping
V28HCC 93 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.175V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.307ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000RxHCCHCC 82 — Systemic Sclerosis (Scleroderma)
0.000What This Code Means
Systemic sclerosis with muscle weakness and inflammation, affecting the patient's strength and mobility.
Coding Tips
- •Distinguish between myopathy (muscle disease) and myositis (muscle inflammation) in documentation
- •Document severity of muscle weakness and functional impact for clinical assessment
Clinical Significance
Systemic sclerosis with myopathy represents scleroderma complicated by muscle weakness and inflammation, significantly impacting patient mobility and quality of life. This combination requires coordinated management addressing both skin/organ fibrosis and muscle involvement.
Documentation Requirements
- ✓Clinical evidence of systemic sclerosis
- ✓Documentation of muscle weakness or inflammation
- ✓Muscle enzyme elevation (CK, aldolase)
- ✓Muscle biopsy or EMG findings if available
- ✓Assessment of functional impairment
- ✓Skin involvement documentation
- ✓Organ involvement assessment
- ✓Treatment response in both muscle and skin
Commonly Confused Codes
M34.89 — Other systemic sclerosis (without specific myopathy)M33.90 — Dermatopolymyositis, unspecified, organ involvement unspecified (primary myositis)M34.9 — Systemic sclerosis, unspecified (less specific)G72.9 — Myopathy, unspecified (isolated muscle disease)M79.3 — Panniculitis, unspecified (different inflammatory process)
Code Hierarchy
└M34Systemic sclerosis [scleroderma]└M34.8Other forms of systemic sclerosis└M34.82Systemic sclerosis with myopathy
└M34.82Systemic sclerosis with myopathy