M33.02
BillableJuvenile dermatomyositis with myopathy
HCC Category Mapping
V28HCC 93 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.175V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.307ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000RxHCCHCC 83 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000What This Code Means
Juvenile dermatomyositis with muscle weakness and inflammation (myopathy) as a primary feature.
Coding Tips
- •Myopathy is a key feature of dermatomyositis; this code specifically captures muscle involvement in children
- •Document muscle weakness severity and affected muscle groups for complete clinical picture
Clinical Significance
Juvenile dermatomyositis with myopathy indicates significant muscle involvement requiring physical therapy, rehabilitation services, and careful monitoring for functional decline. This manifestation often determines treatment intensity and long-term prognosis in pediatric patients.
Documentation Requirements
- ✓Confirmed juvenile dermatomyositis diagnosis
- ✓Documentation of muscle weakness or myopathy
- ✓Muscle enzyme levels (CK, aldolase, LDH)
- ✓EMG/NCV studies if performed
- ✓Muscle biopsy results when available
- ✓Functional assessment of muscle strength
- ✓Physical therapy evaluation and plan
- ✓Treatment response and monitoring plan
Commonly Confused Codes
Code Hierarchy
└M33Dermatopolymyositis└M33.0Juvenile dermatomyositis└M33.02Juvenile dermatomyositis with myopathy
└M33.02Juvenile dermatomyositis with myopathy