M31.4

Billable

Aortic arch syndrome [Takayasu]

HCC Category Mapping

V28HCC 93 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.175

V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.307

ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease

0.000

RxHCCHCC 84 — Vasculitis and Other Autoimmune Disorders

0.000

What This Code Means

A chronic inflammatory disease that narrows the aorta (main artery from the heart) and its branches, causing reduced blood flow to the arms and head.

Coding Tips

•Document which vessels are affected (subclavian, carotid, etc.)
•Note any complications such as hypertension or stroke

Clinical Significance

Takayasu arteritis is a chronic inflammatory disease affecting the aorta and its major branches, primarily occurring in young women. The condition can lead to arterial stenosis, occlusion, and aneurysms, requiring lifelong monitoring and treatment to prevent cardiovascular complications.

Documentation Requirements

✓Clinical evidence of large vessel arteritis
✓Imaging showing aortic or branch vessel involvement
✓Documentation of age at onset (typically under 40)
✓Assessment of vascular stenosis or occlusion
✓Blood pressure measurements in multiple extremities
✓Evidence of systemic inflammation
✓Treatment response monitoring
✓Cardiovascular complication assessment

Commonly Confused Codes

I25.10 — Atherosclerotic heart disease of native coronary artery without angina (atherosclerotic vs inflammatory)I77.6 — Arteritis, unspecified (less specific)M31.5 — Giant cell arteritis with polymyalgia rheumatica (different large vessel arteritis)I70.90 — Unspecified atherosclerosis (degenerative vs inflammatory)Q25.1 — Coarctation of aorta (congenital vs acquired)

Code Hierarchy

└M31Other necrotizing vasculopathies └M31.4Aortic arch syndrome [Takayasu]

└M31.4Aortic arch syndrome [Takayasu]