M06.1
BillableAdult-onset Still's disease
HCC Category Mapping
V28HCC 93 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.175V24HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.307ESRDHCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000RxHCCHCC 83 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
0.000What This Code Means
A rare form of arthritis that begins in adulthood and includes fever, rash, and joint inflammation, often without the typical rheumatoid markers.
Coding Tips
- •This diagnosis requires documentation of systemic features including fever and characteristic rash in addition to arthritis
- •Confirm this is adult-onset (typically age 16 or older) to distinguish from juvenile-onset Still's disease
Clinical Significance
Adult-onset Still's disease is a rare systemic inflammatory disorder characterized by high spiking fevers, arthritis, and salmon-colored rash. This diagnosis indicates a complex multi-system disease requiring specialized rheumatologic care and immunosuppressive therapy.
Documentation Requirements
- ✓Clinical diagnosis of Adult-onset Still's disease by rheumatologist
- ✓Documentation of characteristic triad: fever, arthritis, and rash
- ✓Laboratory findings supporting diagnosis (elevated ferritin, ESR, CRP)
- ✓Exclusion of infectious, malignant, and other inflammatory conditions
- ✓Evidence of systemic manifestations (hepatomegaly, splenomegaly, lymphadenopathy)
- ✓Treatment history with corticosteroids, DMARDs, or biologics
- ✓Assessment of disease activity and organ involvement
- ✓Documentation of adult onset (not juvenile Still's disease)
Excludes 1 — Do NOT code together
- Still's disease NOS (M08.2-)