I82.0
BillableBudd-Chiari syndrome
HCC Category Mapping
V28HCC 267 — Vascular Disease
0.356V24HCC 108 — Vascular Disease
0.297ESRDHCC 108 — Vascular Disease
0.000RxHCCHCC 215 — Pulmonary Embolism and Other Vascular Disease
0.000What This Code Means
A rare condition where blood clots form in the hepatic veins that drain blood from the liver, causing liver congestion and potential liver failure.
Coding Tips
- •This is a serious condition; ensure documentation includes any associated symptoms such as abdominal pain, ascites, or hepatomegaly
- •Investigate and document underlying causes such as myeloproliferative disorders, malignancy, or thrombophilia
Clinical Significance
Budd-Chiari syndrome is a rare but life-threatening condition caused by hepatic vein thrombosis that leads to hepatic congestion, portal hypertension, and potential liver failure. It carries significant implications for risk adjustment as it reflects severe vascular disease requiring ongoing specialist management, anticoagulation, and potentially liver transplant evaluation. Accurate capture ensures appropriate resource allocation for these medically complex patients.
Documentation Requirements
- ✓Clinical diagnosis of Budd-Chiari syndrome documented by hepatologist or treating provider
- ✓Imaging confirmation (Doppler ultrasound, CT, MRI, or venography) showing hepatic vein obstruction
- ✓Documentation of underlying etiology (myeloproliferative disorder, hypercoagulable state, malignancy, etc.)
- ✓Evidence of hepatic complications such as ascites, hepatomegaly, or liver function abnormalities
- ✓Current treatment plan including anticoagulation, diuretics, or consideration for TIPS or transplant
Commonly Confused Codes
K76.5 — Hepatic veno-occlusive disease; involves sinusoidal obstruction syndrome rather than hepatic vein thrombosisI81 — Portal vein thrombosis; involves the portal vein rather than the hepatic veinsI82.210/I82.211 — Superior vena cava thrombosis; involves SVC rather than hepatic veinsK72.0x — Acute and subacute hepatic failure; may be a complication of Budd-Chiari but is coded separatelyI82.890/I82.891 — Embolism and thrombosis of other specified veins; use for venous thrombosis not classified elsewhere