I77.3
BillableArterial fibromuscular dysplasia
HCC Category Mapping
V24HCC 108 — Vascular Disease
0.297ESRDHCC 108 — Vascular Disease
0.000What This Code Means
A genetic condition where the muscular layer of arteries develops abnormally, causing irregular narrowing and widening of the vessel that can restrict blood flow.
Coding Tips
- •Specify the affected artery location (renal, carotid, etc.) when documented
- •This is often discovered incidentally during imaging for other conditions
Clinical Significance
Arterial fibromuscular dysplasia is a non-atherosclerotic, non-inflammatory vascular disease causing abnormal cell growth in artery walls, leading to stenosis, aneurysm, or dissection. Most commonly affecting the renal and carotid arteries, it is a significant cause of secondary hypertension and stroke in younger patients, particularly women. Accurate coding is essential as this represents a distinct vascular pathology requiring specific management.
Documentation Requirements
- ✓Documentation of fibromuscular dysplasia diagnosis
- ✓Affected artery or arteries (renal, carotid, vertebral, iliac, others)
- ✓Imaging findings (classic 'string of beads' appearance on angiography)
- ✓Type classification when documented (medial fibroplasia is most common)
- ✓Associated complications (hypertension, dissection, aneurysm)
- ✓Treatment plan (antihypertensives, antiplatelet therapy, angioplasty if indicated)
Commonly Confused Codes
I77.1 — Stricture of artery: non-specific arterial stricture — use I77.3 when fibromuscular dysplasia is documentedI70.x — Atherosclerosis: atherosclerotic stenosis is a fundamentally different pathologyI72.0 — Aneurysm of carotid artery: aneurysm secondary to fibromuscular dysplasia should code both conditionsI72.2 — Aneurysm of renal artery: renal artery aneurysm from fibromuscular dysplasia should code both
Code Hierarchy
└I77Other disorders of arteries and arterioles└I77.3Arterial fibromuscular dysplasia
└I77.3Arterial fibromuscular dysplasia