I42.1
BillableObstructive hypertrophic cardiomyopathy
HCC Category Mapping
V28HCC 227 — Cardiomyopathy
0.339V24HCC 85 — Congestive Heart Failure
0.368ESRDHCC 85 — Congestive Heart Failure
0.000RxHCCHCC 186 — Heart Failure
0.000What This Code Means
A condition where the heart muscle becomes abnormally thick, particularly in the wall between the two lower chambers, which can obstruct blood flow out of the heart.
Coding Tips
- •Document whether the patient has symptoms such as chest pain, shortness of breath, or syncope
- •Note any family history of sudden cardiac death or hypertrophic cardiomyopathy
Clinical Significance
Obstructive hypertrophic cardiomyopathy is a genetic heart condition causing asymmetric thickening of the interventricular septum that obstructs left ventricular outflow. It is the most common cause of sudden cardiac death in young athletes. This condition requires lifelong monitoring, activity restrictions, and may necessitate septal reduction therapy or implantable cardioverter defibrillator placement.
Documentation Requirements
- ✓Provider diagnosis of obstructive hypertrophic cardiomyopathy
- ✓Echocardiographic findings showing asymmetric septal hypertrophy with left ventricular outflow tract obstruction
- ✓Left ventricular outflow tract gradient documented
- ✓Family history of hypertrophic cardiomyopathy or sudden cardiac death
- ✓Symptoms (exertional dyspnea, syncope, chest pain) and functional status
Commonly Confused Codes
I42.2 — Other hypertrophic cardiomyopathy; non-obstructive form without outflow tract obstructionI42.0 — Dilated cardiomyopathy; enlarged and weakened heart, not thickenedI11.0 — Hypertensive heart disease with heart failure; hypertensive cardiac hypertrophy is differentI42.9 — Cardiomyopathy, unspecified; use only when the type is not documented
Code Hierarchy
└I42Cardiomyopathy└I42.1Obstructive hypertrophic cardiomyopathy
└I42.1Obstructive hypertrophic cardiomyopathy