I27.1
BillableKyphoscoliotic heart disease
HCC Category Mapping
V28HCC 226 — Heart Failure, Specified
0.000V24HCC 85 — Congestive Heart Failure
0.368ESRDHCC 85 — Congestive Heart Failure
0.000RxHCCHCC 184 — Pulmonary Hypertension, Other
0.000What This Code Means
Heart disease caused by severe spinal curvature that compresses the lungs and increases strain on the heart.
Coding Tips
Clinical Significance
Kyphoscoliotic heart disease represents cardiac complications arising from severe spinal deformity that restricts lung expansion. This condition reflects multi-system disease complexity requiring management of both musculoskeletal and cardiopulmonary problems. It is relatively uncommon and indicates significant chronic disease burden.
Documentation Requirements
- ✓Documented diagnosis of kyphoscoliotic heart disease
- ✓Underlying kyphoscoliosis with severity documented (degree of curvature)
- ✓Evidence of cardiac involvement (right heart strain, cor pulmonale, heart failure symptoms)
- ✓Pulmonary function testing showing restrictive pattern
- ✓Echocardiogram or other cardiac imaging findings
Commonly Confused Codes
I27.81 — Cor pulmonale (chronic); broader category of right heart disease from lung diseaseI27.0 — Primary pulmonary hypertension; not caused by spinal deformityM41.9 — Scoliosis, unspecified; code the spinal condition separately, not interchangeablyI27.89 — Other specified pulmonary heart diseases; use when the pulmonary heart disease is not kyphoscoliotic in nature
Code Hierarchy
└I27Other pulmonary heart diseases└I27.1Kyphoscoliotic heart disease
└I27.1Kyphoscoliotic heart disease