What is ICD-10 code G71.035?

G71.035 is the ICD-10-CM diagnosis code for Limb girdle muscular dystrophy due to anoctamin-5 dysfunction. A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by anoctamin-5 protein dysfunction, which is involved in muscle calcium regulation. G71.035 is a billable code, meaning it can be reported on a claim as a primary or secondary diagnosis when supported by documentation. G71.035 is part of the FY2026 ICD-10-CM code set published by the CMS National Center for Health Statistics and used on Medicare, Medicaid, and commercial claims in the United States.

Yes. G71.035 is a billable ICD-10-CM code that can be reported on professional and institutional claims as a primary or secondary diagnosis when the provider documentation supports the specific condition described. Billable codes in ICD-10-CM are coded to the highest level of specificity available for the documented diagnosis. G71.035 is current for fiscal year 2026 and remains in the active CMS ICD-10-CM code set published by the National Center for Health Statistics.

What is the V28 vs V24 difference for G71.035?

CMS phased in the V28 risk adjustment model over payment years 2024 (33%), 2025 (67%), and 2026 (100%), replacing V24. V28 consolidates HCC categories, removes some lower-acuity conditions, and recalibrates RAF weights across the entire model. For G71.035, V28 maps to Muscular Dystrophy at RAF 0.000 while V24 mapped to Muscular Dystrophy at RAF 0.358. Both models can still appear in legacy data and in payer-specific lookback periods.

What should coders know when reporting G71.035?

Confirm anoctamin-5 gene mutation through genetic testing before coding this specific subtype Note that anoctamin-5 deficiency can present with variable muscle involvement patterns Because G71.035 maps to a payment HCC, the documentation must also satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's risk adjustment score.

G71.035 ICD-10 Code: Limb girdle muscular

ICD-10-CM Code View

HCC Buddy Code Card

Digital ICD-10 code-book layout with official code detail, always-visible risk models, Code Trumping, and Buddy coding guidance.

Code lookupG71.035Effective periodFY2026 Apr Update (Apr 1-Sep 30)

FY 2026 Apr update / Diseases of the nervous system (G00-G99) / Diseases of myoneural junction and muscle (G70-G73)

G71.035

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Limb girdle muscular dystrophy due to anoctamin-5 dysfunction

A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by anoctamin-5 protein dysfunction, which is involved in muscle calcium regulation.

Buddy Insight

Limb girdle muscular dystrophy due to anoctamin-5 dysfunction (LGMD2L/LGMDR12) is an increasingly recognized form of limb girdle dystrophy involving a calcium-activated chloride channel protein.

CMS-HCC V28

Mapped

HCC 197

Muscular Dystrophy

RAF 0.0

CMS-HCC V24

Mapped

HCC 76

Muscular Dystrophy

RAF 0.358

ACA/HHS

Not risk-adjusted for this model/period.

RAF 0

ESRD/PACE

Mapped

HCC 76

Muscular Dystrophy

RAF 0.0

RXHCC

Not risk-adjusted for this model/period.

RAF 0

Code Trumping

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Compare selected patient codes to show trumped or trumps impact.

Code Book Path

Official

G71.0Muscular dystrophy

G71.03Limb girdle muscular dystrophies

G71.035Limb girdle muscular dystrophy due to anoctamin-5 dysfunction

Inclusion Terms

Official

Anoctamin-5-related LGMD R12
Anoctaminopathy
Autosomal recessive limb girdle muscular dystrophy type 2L
Miyoshi myopathy type 3

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for G71.035 in this effective period.

Related Child Codes

Official

G71.031Autosomal dominant limb girdle muscular dystrophy

G71.032Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction

G71.033Limb girdle muscular dystrophy due to dysferlin dysfunction

G71.034Limb girdle muscular dystrophy due to sarcoglycan dysfunction

G71.036Limb girdle muscular dystrophy due to fukutin related protein dysfunction

Includes

Official

ICD-10-CM does not list Includes notes for G71.035 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for G71.035 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for G71.035 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for G71.035 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for G71.035 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance

Genetic testing confirming ANO5 gene mutation

Clinical presentation: adult-onset proximal weakness, elevated creatine kinase

Age of onset and progression pattern

Muscle biopsy findings when available

MEAT Support

HCC Buddy guidance

Genetic testing confirming ANO5 gene mutation

Clinical presentation: adult-onset proximal weakness, elevated creatine kinase

Age of onset and progression pattern

Muscle biopsy findings when available

Audit Caution

HCC Buddy guidance

Using the unspecified limb girdle code when genetic testing confirms anoctamin-5 mutation

Not recognizing that anoctamin-5 deficiency can present with asymmetric weakness, which is atypical for muscular dystrophies

Confusing with dysferlin-related or calpain-3-related dystrophies based on clinical similarity

Failing to update coding when genetic results become available

Common Mistakes

HCC Buddy guidance

G71.033 — Dysferlin dysfunction can have overlapping clinical features but involves a different protein

G71.032 — Calpain-3 dysfunction also presents with proximal weakness in adulthood

G71.039 — Limb girdle muscular dystrophy, unspecified should not be used when anoctamin-5 mutation is confirmed

G71.038 — Other limb girdle muscular dystrophy is for identified subtypes without their own specific code

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Is G71.035 an HCC code?

Yes. G71.035 maps to Muscular Dystrophy under the CMS-HCC V28 risk adjustment model (and Muscular Dystrophy under V24).

HCC Category Mapping

V28HCC 197, Muscular Dystrophy

0.000

V24HCC 76, Muscular Dystrophy

0.358

ESRDHCC 76, Muscular Dystrophy

0.000

RAF weights shown are the community, non-dual, aged base weights from the CMS risk adjustment model file. Actual per-patient RAF contribution depends on member segment, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains in use during the transition and for historical data.

MEAT Criteria for G71.035

For G71.035to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.

MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
EEvaluate: test results, medication response, or physical findings reviewed by the provider
AAssess: explicit mention in the assessment or plan with acknowledgment of status
TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed G71.035 during that encounter, not just copy-forwarded from a problem list.

What This Code Means

G71.035 is the ICD-10-CM diagnosis code for limb girdle muscular dystrophy due to anoctamin-5 dysfunction. A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by anoctamin-5 protein dysfunction, which is involved in muscle calcium regulation. G71.035 sits in the ICD-10-CM chapter for diseases of the nervous system (g00-g99), within the section covering diseases of myoneural junction and muscle (g70-g73).

Under the CMS-HCC V28 risk adjustment model, G71.035 maps to Muscular Dystrophy (HCC 197) with a community, non-dual, aged base RAF weight of 0.000. Under the older V24 model, G71.035 mapped to the same category but with a base RAF weight of 0.358, V28 recalibrated weights across the entire model. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition.

Confirm anoctamin-5 gene mutation through genetic testing before coding this specific subtype. Because G71.035 maps to a payment HCC, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's Medicare Advantage risk adjustment score. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for G71.035 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

•Confirm anoctamin-5 gene mutation through genetic testing before coding this specific subtype
•Note that anoctamin-5 deficiency can present with variable muscle involvement patterns

Clinical Significance

Limb girdle muscular dystrophy due to anoctamin-5 dysfunction (LGMD2L/LGMDR12) is an increasingly recognized form of limb girdle dystrophy involving a calcium-activated chloride channel protein. It typically presents in adulthood with milder proximal weakness and elevated creatine kinase. Accurate coding is important as this subtype has distinct prognostic features and potential therapeutic implications.

Documentation Requirements

✓Genetic testing confirming ANO5 gene mutation
✓Clinical presentation: adult-onset proximal weakness, elevated creatine kinase
✓Age of onset and progression pattern
✓Muscle biopsy findings when available
✓Functional assessment: walking ability, arm strength, respiratory function
✓Provider's explicit diagnosis specifying anoctamin-5 dysfunction

Commonly Confused Codes

•G71.033: Dysferlin dysfunction can have overlapping clinical features but involves a different protein
•G71.032: Calpain-3 dysfunction also presents with proximal weakness in adulthood
•G71.039: Limb girdle muscular dystrophy, unspecified should not be used when anoctamin-5 mutation is confirmed
•G71.038: Other limb girdle muscular dystrophy is for identified subtypes without their own specific code