What is ICD-10 code G71.033?

G71.033 is the ICD-10-CM diagnosis code for Limb girdle muscular dystrophy due to dysferlin dysfunction. A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by dysferlin protein dysfunction, which helps stabilize muscle cell membranes. G71.033 is a billable code, meaning it can be reported on a claim as a primary or secondary diagnosis when supported by documentation. G71.033 is part of the FY2026 ICD-10-CM code set published by the CMS National Center for Health Statistics and used on Medicare, Medicaid, and commercial claims in the United States.

Yes. G71.033 is a billable ICD-10-CM code that can be reported on professional and institutional claims as a primary or secondary diagnosis when the provider documentation supports the specific condition described. Billable codes in ICD-10-CM are coded to the highest level of specificity available for the documented diagnosis. G71.033 is current for fiscal year 2026 and remains in the active CMS ICD-10-CM code set published by the National Center for Health Statistics.

What is the V28 vs V24 difference for G71.033?

CMS phased in the V28 risk adjustment model over payment years 2024 (33%), 2025 (67%), and 2026 (100%), replacing V24. V28 consolidates HCC categories, removes some lower-acuity conditions, and recalibrates RAF weights across the entire model. For G71.033, V28 maps to Muscular Dystrophy at RAF 0.000 while V24 mapped to Muscular Dystrophy at RAF 0.358. Both models can still appear in legacy data and in payer-specific lookback periods.

What should coders know when reporting G71.033?

Verify dysferlin gene mutation or protein deficiency through genetic or muscle biopsy testing Note that dysferlin-related disorders can present with variable severity and age of onset Because G71.033 maps to a payment HCC, the documentation must also satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's risk adjustment score.

G71.033 ICD-10 Code: Limb girdle muscular

ICD-10-CM Code View

HCC Buddy Code Card

Digital ICD-10 code-book layout with official code detail, always-visible risk models, Code Trumping, and Buddy coding guidance.

Code lookupG71.033Effective periodFY2026 Apr Update (Apr 1-Sep 30)

FY 2026 Apr update / Diseases of the nervous system (G00-G99) / Diseases of myoneural junction and muscle (G70-G73)

G71.033

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Limb girdle muscular dystrophy due to dysferlin dysfunction

A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by dysferlin protein dysfunction, which helps stabilize muscle cell membranes.

Buddy Insight

CMS-HCC V28

Mapped

HCC 197

Muscular Dystrophy

RAF 0.0

CMS-HCC V24

Mapped

HCC 76

Muscular Dystrophy

RAF 0.358

ACA/HHS

Not risk-adjusted for this model/period.

RAF 0

ESRD/PACE

Mapped

HCC 76

Muscular Dystrophy

RAF 0.0

RXHCC

Not risk-adjusted for this model/period.

RAF 0

Code Trumping

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Compare selected patient codes to show trumped or trumps impact.

Code Book Path

Official

G71.0Muscular dystrophy

G71.03Limb girdle muscular dystrophies

G71.033Limb girdle muscular dystrophy due to dysferlin dysfunction

Inclusion Terms

Official

Dysferlinopathy
LGMD R2 dysferlin-related
Limb girdle muscular dystrophy type 2B
Miyoshi Myopathy type 1

Excludes 2

Official

ICD-10-CM does not list Excludes 2 notes for G71.033 in this effective period.

Related Child Codes

Official

G71.031Autosomal dominant limb girdle muscular dystrophy

G71.032Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction

G71.034Limb girdle muscular dystrophy due to sarcoglycan dysfunction

G71.035Limb girdle muscular dystrophy due to anoctamin-5 dysfunction

G71.036Limb girdle muscular dystrophy due to fukutin related protein dysfunction

Includes

Official

ICD-10-CM does not list Includes notes for G71.033 in this effective period.

Excludes 1

Official

ICD-10-CM does not list Excludes 1 notes for G71.033 in this effective period.

Code First

Official

ICD-10-CM does not list Code First sequencing instructions for G71.033 in this effective period.

Use Additional

Official

ICD-10-CM does not list Use Additional Code instructions for G71.033 in this effective period.

Code Also

Official

ICD-10-CM does not list Code Also instructions for G71.033 in this effective period.

Buddy Documentation Tip

HCC Buddy guidance

Genetic testing confirming DYSF gene mutation or muscle biopsy showing absent/reduced dysferlin

Clinical presentation: proximal weakness, possible distal involvement, elevated creatine kinase

Age of onset documentation (typically late teens to young adulthood)

Functional assessment: ambulatory status, specific muscle groups affected

MEAT Support

HCC Buddy guidance

Genetic testing confirming DYSF gene mutation or muscle biopsy showing absent/reduced dysferlin

Clinical presentation: proximal weakness, possible distal involvement, elevated creatine kinase

Age of onset documentation (typically late teens to young adulthood)

Functional assessment: ambulatory status, specific muscle groups affected

Audit Caution

HCC Buddy guidance

Not recognizing that dysferlinopathy can present as Miyoshi myopathy with distal weakness, which may be mistaken for a non-dystrophic condition

Using the unspecified limb girdle code when genetic testing has confirmed dysferlin mutation

Confusing with calpain-3 dysfunction due to overlapping clinical features

Failing to update coding when genetic results return confirming the specific subtype

Common Mistakes

HCC Buddy guidance

G71.032 — Limb girdle muscular dystrophy due to calpain-3 dysfunction has similar proximal weakness but different protein deficiency

G71.0340 — Limb girdle muscular dystrophy due to sarcoglycan dysfunction involves a different structural protein

G71.039 — Limb girdle muscular dystrophy, unspecified should not be used when dysferlin mutation is confirmed

G71.09 — Other specified muscular dystrophies is less specific

Last updated: FY2026 ICD-10-CM Apr update, Apr 1, 2026 through Sep 30, 2026. CMS-HCC V28 is 100% phased in for payment year 2026.

Is G71.033 an HCC code?

Yes. G71.033 maps to Muscular Dystrophy under the CMS-HCC V28 risk adjustment model (and Muscular Dystrophy under V24).

HCC Category Mapping

V28HCC 197, Muscular Dystrophy

0.000

V24HCC 76, Muscular Dystrophy

0.358

ESRDHCC 76, Muscular Dystrophy

0.000

RAF weights shown are the community, non-dual, aged base weights from the CMS risk adjustment model file. Actual per-patient RAF contribution depends on member segment, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains in use during the transition and for historical data.

MEAT Criteria for G71.033

For G71.033to count as a valid HCC diagnosis in a given encounter, the provider's documentation must show MEAT: Monitor, Evaluate, Assess, or Treat. A diagnosis from a prior year does not carry forward automatically, it has to be re-documented and supported each calendar year.

MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
EEvaluate: test results, medication response, or physical findings reviewed by the provider
AAssess: explicit mention in the assessment or plan with acknowledgment of status
TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Only one of M/E/A/T is required to support the code, but the documentation must be specific enough to show that the provider actually addressed G71.033 during that encounter, not just copy-forwarded from a problem list.

What This Code Means

G71.033 is the ICD-10-CM diagnosis code for limb girdle muscular dystrophy due to dysferlin dysfunction. A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by dysferlin protein dysfunction, which helps stabilize muscle cell membranes. G71.033 sits in the ICD-10-CM chapter for diseases of the nervous system (g00-g99), within the section covering diseases of myoneural junction and muscle (g70-g73).

Under the CMS-HCC V28 risk adjustment model, G71.033 maps to Muscular Dystrophy (HCC 197) with a community, non-dual, aged base RAF weight of 0.000. Under the older V24 model, G71.033 mapped to the same category but with a base RAF weight of 0.358, V28 recalibrated weights across the entire model. V28 is the CMS-HCC risk adjustment model that reached 100% phase-in for payment year 2026, replacing V24 which was used during the PY2024–PY2025 transition.

Verify dysferlin gene mutation or protein deficiency through genetic or muscle biopsy testing. Because G71.033 maps to a payment HCC, the provider's documentation must satisfy MEAT criteria (Monitor, Evaluate, Assess, or Treat) for the encounter to count toward the patient's Medicare Advantage risk adjustment score. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.

HCC Buddy maintains structured V28 and V24 mapping, RAF weights, and MEAT documentation criteria for G71.033 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

•Verify dysferlin gene mutation or protein deficiency through genetic or muscle biopsy testing
•Note that dysferlin-related disorders can present with variable severity and age of onset

Clinical Significance

Limb girdle muscular dystrophy due to dysferlin dysfunction (LGMD2B/LGMDR2, also known as dysferlinopathy or Miyoshi myopathy) affects muscle membrane repair, leading to progressive proximal and sometimes distal weakness. It is unique among muscular dystrophies in that it can present with distal weakness initially. Accurate coding supports genetic counseling, potential therapeutic trial eligibility, and appropriate risk adjustment.

Documentation Requirements

✓Genetic testing confirming DYSF gene mutation or muscle biopsy showing absent/reduced dysferlin
✓Clinical presentation: proximal weakness, possible distal involvement, elevated creatine kinase
✓Age of onset documentation (typically late teens to young adulthood)
✓Functional assessment: ambulatory status, specific muscle groups affected
✓Family history and inheritance pattern (autosomal recessive)
✓Provider's explicit diagnosis specifying dysferlin dysfunction

Commonly Confused Codes

•G71.032: Limb girdle muscular dystrophy due to calpain-3 dysfunction has similar proximal weakness but different protein deficiency
•G71.0340: Limb girdle muscular dystrophy due to sarcoglycan dysfunction involves a different structural protein
•G71.039: Limb girdle muscular dystrophy, unspecified should not be used when dysferlin mutation is confirmed
•G71.09: Other specified muscular dystrophies is less specific