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G71.032 ICD-10-CM Code: Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction

G71.032 maps to CMS-HCC V28 197. A source-labeled RAF reference is available. Confirm the documented diagnosis and applicable coding requirements. MEAT criteria · RAF Calculator · HCC coding software

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Code lookupG71.032

FY 2026 Apr update / Diseases of the nervous system (G00-G99) / Diseases of myoneural junction and muscle (G70-G73)

G71.032

Billable / SpecificICD-10-CMOfficial ICD-10-CMCodebook guidance

Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction

A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by calpain-3 protein dysfunction, inherited in an autosomal recessive pattern requiring two mutated gene copies.

Buddy the Bee presenting code insight

Buddy Insight

Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction (LGMD2A/LGMDR1) is one of the most common forms of limb girdle muscular dystrophy.

CMS-HCC V28

HCC 197

Code-level coefficient reference

CMS-HCC V24

Historical

Historical

Not used for CY2026 payment

ACA/HHS

HCC 117

Code-level coefficient reference

ESRD/PACE

HCC 76

Code-level coefficient reference

RXHCC

N/A

Not mapped

Inclusion Terms

Official
  • Limb girdle muscular dystrophy type 2A
  • LGMD R1 calpain-3-related
  • Primary calpainopathy

Excludes 2

Official
  • certain conditions originating in the perinatal period (P04-P96)Inherited from G00-G99, G71
  • certain infectious and parasitic diseases (A00-B99)Inherited from G00-G99, G71
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)Inherited from G00-G99, G71
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)Inherited from G00-G99, G71
  • endocrine, nutritional and metabolic diseases (E00-E88)Inherited from G00-G99, G71
  • injury, poisoning and certain other consequences of external causes (S00-T88)Inherited from G00-G99, G71
  • neoplasms (C00-D49)Inherited from G00-G99, G71
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)Inherited from G00-G99, G71
  • arthrogryposis multiplex congenita (Q74.3)Inherited from G00-G99, G71
  • metabolic disorders (E70-E88)Inherited from G00-G99, G71
  • myositis (M60.-)Inherited from G00-G99, G71

Includes

Official

No Includes notes are included in this display for G71.032. Check the code and parent instructions in the Code Book.

Excludes 1

Official

No Excludes 1 notes are included in this display for G71.032. Check the code and parent instructions in the Code Book.

Code First

Official

No Code First sequencing instructions are included in this display for G71.032. Check the code and parent instructions in the Code Book.

Use Additional

Official

No Use Additional Code instructions are included in this display for G71.032. Check the code and parent instructions in the Code Book.

Code Also

Official

No Code Also instructions are included in this display for G71.032. Check the code and parent instructions in the Code Book.

Buddy Documentation Tip

HCC Buddy guidance
Genetic testing confirming CAPN3 gene mutation causing calpain-3 deficiency
Clinical presentation: proximal weakness, elevated creatine kinase
Muscle biopsy showing reduced or absent calpain-3 on Western blot when available
Autosomal recessive inheritance pattern documentation

MEAT Support

HCC Buddy guidance
Genetic testing confirming CAPN3 gene mutation causing calpain-3 deficiency
Clinical presentation: proximal weakness, elevated creatine kinase
Muscle biopsy showing reduced or absent calpain-3 on Western blot when available
Autosomal recessive inheritance pattern documentation

Audit Caution

HCC Buddy guidance
Coding as unspecified limb girdle muscular dystrophy when genetic testing has identified the calpain-3 mutation
Confusing calpain-3 dysfunction with dysferlin dysfunction, which have similar clinical presentations but different genetic causes
Not updating the code from unspecified to specific when genetic test results return during the care episode
Failing to capture both the carrier status in family members and the disease in affected individuals

Common Mistakes

HCC Buddy guidance
G71.031 — Autosomal dominant limb girdle muscular dystrophy has a different inheritance pattern
G71.033 — Limb girdle muscular dystrophy due to dysferlin dysfunction involves a different protein deficiency
G71.039 — Limb girdle muscular dystrophy, unspecified should not be used when calpain-3 mutation is confirmed
G71.038 — Other limb girdle muscular dystrophy is for identified subtypes without their own code, not for calpain-3

Current with CMS: FY2026 ICD-10-CM Apr 1 update (effective Apr 1 – Sep 30, 2026) · CMS-HCC V28, 100% phased in for payment year 2026. FY2027 code set already staged for October 1, 2026. How HCC Buddy stays current →

Is G71.032 an HCC code?

Yes. G71.032 (Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction) maps to HCC 197, Muscular Dystrophy under the CMS-HCC V28 risk adjustment model, with a source-labeled community non-dual aged reference coefficient of 0.426. Source-labeled code-level coefficients are references, not member totals. Actual contribution depends on complete member context, hierarchy and cleanup rules, interactions, and model year. HCC Buddy's RAF Calculator supports CMS-HCC V28 PY2026 and shows no score unless every required source and calculation check passes. It is billable for payment year 2026.

Coder answer: G71.032 is billable and maps to V28 HCC 197, Muscular Dystrophy. Open it in the Code Book for the tabular path, RAF, and MEAT checklist.

Code
G71.032
Description
Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
HCC (V28)
HCC 197 — Muscular Dystrophy
RAF reference coefficient
0.426
Billable
Yes
Payment year
2026

HCC Category Mapping

V28HCC 197, Muscular Dystrophy
0.426
ESRDHCC 76, Muscular Dystrophy
Not separately weighted

These are source-labeled model coefficients, not member totals. A category may still be removed by hierarchy or model cleanup rules. Weights are not directly comparable across models: CMS-HCC V28 and V24 use Community, Non-Dual, Aged; ESRD uses the dialysis continuing-enrollee model; RxHCC is the Part D continuing-enrollee, non-low-income, aged weight (a larger scale than CMS-HCC). ACA/HHS has no single weight — it varies by metal level. Actual per-patient RAF contribution depends on member context, hierarchy and cleanup rules, interactions, and the model year used by the payer. V28 is the CMS-HCC model phased in over payment years 2024–2026; V24 remains available for historical review.

Work G71.032 in the Code Book — tabular path, V28 RAF reference, and MEAT checklist →

MEAT review for G71.032

For G71.032, confirm that the documentation supports the diagnosis and meets the applicable coding, encounter, program and payer requirements. MEAT (Monitor, Evaluate, Assess, or Treat) is a review mnemonic, not a universal CMS coding rule.

  • MMonitor: signs, symptoms, disease progression, or lab trending documented in the note
  • EEvaluate: test results, medication response, or physical findings reviewed by the provider
  • AAssess: explicit mention in the assessment or plan with acknowledgment of status
  • TTreat: medication, referral, procedure, therapy, or counseling tied to the diagnosis

Coder workflow notes

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What This Code Means

G71.032 is the ICD-10-CM diagnosis code for autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction. A genetic muscle weakness disorder affecting the hip and shoulder muscles caused by calpain-3 protein dysfunction, inherited in an autosomal recessive pattern requiring two mutated gene copies. G71.032 sits in the ICD-10-CM chapter for diseases of the nervous system (g00-g99), within the section covering diseases of myoneural junction and muscle (g70-g73).

Under the CMS-HCC V28 risk adjustment model, G71.032 maps to Muscular Dystrophy (HCC 197) with a source-labeled community, non-dual, aged reference coefficient of 0.426. No V24 mapping is shown for G71.032; use the applicable model and payment year when reviewing the V28 mapping. For CY2026 non-PACE Medicare Advantage, CMS uses 100% of the 2024 CMS-HCC model (V28). PACE uses a separate model blend. Source-labeled code-level coefficients are references, not member totals. Actual contribution depends on complete member context, hierarchy and cleanup rules, interactions, and model year. HCC Buddy's RAF Calculator supports CMS-HCC V28 PY2026 and shows no score unless every required source and calculation check passes.

Confirm genetic testing results specifically identifying calpain-3 mutations before coding. For G71.032, confirm that the documentation supports the diagnosis and meets the applicable coding, encounter, program and payer requirements. MEAT (Monitor, Evaluate, Assess, or Treat) is a review mnemonic, not a universal CMS coding rule. When documentation is ambiguous, coders should issue a provider query rather than assume the highest-specificity variant.

HCC Buddy maintains structured V28 and V24 mapping, source-labeled coefficient references, and MEAT documentation criteria for G71.032 sourced directly from the CMS-HCC risk adjustment model files and the CMS ICD-10-CM code set.

Coding Tips

  • Confirm genetic testing results specifically identifying calpain-3 mutations before coding
  • Document both parents as carriers if family history is available

Clinical Significance

Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction (LGMD2A/LGMDR1) is one of the most common forms of limb girdle muscular dystrophy. It presents with progressive proximal weakness and elevated creatine kinase, and has specific genetic implications for family counseling. Precise coding enables tracking of this specific genetic subtype and may support eligibility for clinical trials and targeted therapies.

Documentation Requirements

  • Genetic testing confirming CAPN3 gene mutation causing calpain-3 deficiency
  • Clinical presentation: proximal weakness, elevated creatine kinase
  • Muscle biopsy showing reduced or absent calpain-3 on Western blot when available
  • Autosomal recessive inheritance pattern documentation
  • Functional status assessment: ambulation, respiratory function
  • Provider's explicit diagnosis specifying calpain-3 dysfunction

Commonly Confused Codes

  • G71.031: Autosomal dominant limb girdle muscular dystrophy has a different inheritance pattern
  • G71.033: Limb girdle muscular dystrophy due to dysferlin dysfunction involves a different protein deficiency
  • G71.039: Limb girdle muscular dystrophy, unspecified should not be used when calpain-3 mutation is confirmed
  • G71.038: Other limb girdle muscular dystrophy is for identified subtypes without their own code, not for calpain-3

Child Codes

Code Hierarchy

G71.032 code history

Code setChange
FY2023 (effective Oct 1, 2022)Added to the code set

Source: official CMS ICD-10-CM order and addenda files, FY2016 through FY2027.

For G71.032, confirm that the documentation supports the diagnosis and meets the applicable coding, encounter, program and payer requirements. MEAT (Monitor, Evaluate, Assess, or Treat) is a review mnemonic, not a universal CMS coding rule.

G71.032 maps to CMS-HCC V28 category 197, Muscular Dystrophy. See the ICD-10 to HCC mapping hub for how the V28 crosswalk works. The mapping identifies a payment HCC category for G71.032. Review its source-labeled HCC coefficient above, check the RAF Calculator with complete member context for CMS-HCC V28 PY2026, and confirm the documentation the chart needs before the code is submitted. HCC Buddy shows no RAF score unless every required source and calculation check passes.

Work G71.032 in HCC Buddy

Open G71.032 in the Code Book for the full Index-to-Tabular path, MEAT checklist, and V28 HCC mapping, or in the Encoder to code from a keyword search. Pro includes 7 days to try everything, no card required.