G40.C19
BillableLafora progressive myoclonus epilepsy, intractable, without status epilepticus
HCC Category Mapping
V28HCC 201 — Seizure Disorders and Convulsions
0.262V24HCC 79 — Seizure Disorders and Convulsions
0.244ESRDHCC 79 — Seizure Disorders and Convulsions
0.000RxHCCHCC 163 — Seizure Disorders, Intractable Epilepsy
0.000What This Code Means
Lafora disease that does not respond adequately to medication, but the patient is not currently experiencing prolonged or repeated seizure activity.
Coding Tips
- •Confirm intractability is documented and Lafora disease is confirmed through genetic or pathological testing
- •Verify absence of status epilepticus during the encounter or documentation period
Clinical Significance
Lafora progressive myoclonus epilepsy, intractable, without status epilepticus represents the chronic management phase of advanced Lafora disease. The intractable designation is the norm in later-stage Lafora disease as the condition invariably progresses. These patients require ongoing palliative seizure management, supportive care, and multidisciplinary support for progressive cognitive and motor decline.
Documentation Requirements
- ✓Confirmed Lafora disease diagnosis (genetic or pathological)
- ✓Documentation of intractability
- ✓Absence of status epilepticus at the encounter
- ✓Current disease stage and functional status
- ✓Medication regimen for seizure mitigation
- ✓Palliative care and support services documentation
Commonly Confused Codes
G40.C09 — Lafora disease, NOT intractable; early-stage presentationG40.C11 — Lafora disease, intractable, WITH status epilepticusG40.B19 — Juvenile myoclonic epilepsy, intractable; non-progressive conditionG40.804 — Other epilepsy, intractable; less specificG40.834 — Dravet syndrome, intractable; different genetic epilepsy
Code Hierarchy
└G40Epilepsy and recurrent seizures└G40.CLafora progressive myoclonus epilepsy└G40.C1Lafora progressive myoclonus epilepsy, intractable└G40.C19Lafora progressive myoclonus epilepsy, intractable, without status epilepticus
└G40.C19Lafora progressive myoclonus epilepsy, intractable, without status epilepticus