G40.C09
BillableLafora progressive myoclonus epilepsy, not intractable, without status epilepticus
HCC Category Mapping
What This Code Means
Lafora disease is a rare, inherited progressive epilepsy causing myoclonic seizures and neurological decline. This code indicates the condition responds to medication and the patient is not currently experiencing prolonged seizure activity.
Coding Tips
- •Confirm Lafora disease diagnosis through genetic testing or pathological findings in documentation
- •Verify absence of status epilepticus and that seizures are controlled with current treatment
Clinical Significance
Lafora progressive myoclonus epilepsy, medication-responsive, without status epilepticus likely represents early-stage disease when seizures may still respond to treatment. Lafora disease is a devastating progressive condition that typically presents in late childhood or adolescence and leads to intractable epilepsy, cognitive decline, and death within 10 years of onset. Early-stage medication responsiveness is expected to decline over time.
Documentation Requirements
- ✓Confirmed Lafora disease diagnosis through genetic testing or pathology
- ✓Current seizure control status (responding to medication)
- ✓Absence of status epilepticus
- ✓Disease stage and progression timeline
- ✓Current medication regimen
- ✓Genetic counseling documentation for family members